Al-Falahi Abdulqader, Al-Sayyadi Maeen, Al-Ozair Bassam, Alwah Ali, Ahmed Faisal
Department of Radiology, Faculty of Medicine 21st September University of Medical and Applied Sciences Sana'a Yemen.
Department of Radiology 48 Modern Hospital Sana'a Yemen.
Clin Case Rep. 2025 Feb 10;13(2):e70183. doi: 10.1002/ccr3.70183. eCollection 2025 Feb.
Renal angiomyolipoma (AML) are benign tumors incidentally diagnosed during routine radiologic images; nonetheless, AML rupture is uncommon and has been associated with fatal consequences, demanding prompt intervention, especially during pregnancy with symptoms of Wunderlich's syndrome (WS) and atrophied contralateral kidney. We report a 30-year-old pregnant woman who presented with gross hematuria and hypovolemic shock in her seventh month of pregnancy. Magnetic resonance imaging revealed a 15 × 13.5 × 16 cm AML mass in the left kidney, a 5 × 6 cm intrarenal pseudoaneurysm, and a massive retroperitoneal hematoma with an atrophied contralateral right kidney. After achieving hemodynamic stability, selective renal arterial embolization was performed with a successful outcome. She subsequently delivered her baby via cesarean section without complications. In conclusion, although WS due to AML rupture is rare during pregnancy, accurate diagnosis and prompt endovascular treatment should be pursued in cases involving a solitary kidney and associated comorbid conditions to safeguard the lives of both the patient and the baby, stabilize renal function, and prevent catastrophic complications.
肾血管平滑肌脂肪瘤(AML)是在常规影像学检查中偶然发现的良性肿瘤;然而,AML破裂并不常见,且与致命后果相关,需要及时干预,尤其是在怀孕期间出现Wunderlich综合征(WS)症状且对侧肾脏萎缩的情况下。我们报告一例30岁孕妇,在妊娠第七个月出现肉眼血尿和低血容量性休克。磁共振成像显示左肾有一个15×13.5×16cm的AML肿块、一个5×6cm的肾内假性动脉瘤以及巨大的腹膜后血肿,对侧右肾萎缩。在血流动力学稳定后,进行了选择性肾动脉栓塞术,结果成功。她随后通过剖宫产顺利产下婴儿,无并发症。总之,尽管妊娠期间因AML破裂导致的WS很少见,但对于涉及孤立肾和相关合并症的病例,应进行准确诊断并及时进行血管内治疗,以保障患者和婴儿的生命安全,稳定肾功能,预防灾难性并发症。