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孕早期血管平滑肌脂肪瘤假性动脉瘤破裂所致温德利希综合征:1例罕见病例报告

Wunderlich Syndrome due to Ruptured Pseudoaneurysm of Angiomyolipoma in First Trimester: A Rare Case Report.

作者信息

Patil Sunil Raghunath, Pawar Prakash Wamanrao, Sawant Ajit Somaji, Savalia Abhishek Jaysukhbhai, Tamhankar Ashwin Sunil

机构信息

Senior Registrar, Department of Urology, Lokmanya Tilak Municipal Medical College, Sion, Mumbai, Maharashtra, India.

Associate Professor, Department of Urology, Lokmanya Tilak Municipal Medical College and General Hospital, Mumbai, Maharashtra, India.

出版信息

J Clin Diagn Res. 2017 Jun;11(6):PD16-PD18. doi: 10.7860/JCDR/2017/25399.10141. Epub 2017 Jun 1.

Abstract

Angiomyolipoma (AML) is a rare benign tumour of kidney which demonstrates rapid growth during pregnancy due to hormonal stimulation, leading to rupture. Majority of reported ruptured AMLs are in third trimester. We report a case of ruptured angiomyolipoma at 10th week of gestation, the earliest rupture known in singleton pregnancy. The AML had pseudo-aneurysm formation with extra-tumoural rupture during pregnancy, a finding never reported in literature yet. The patient had active bleeding with expanding peri-nephric haematoma during initial two days of conservative management. Hence, after counselling and taking prior informed written consent for Medical Termination of Pregnancy (MTP), computed tomography scan of abdomen with angiography followed by emergency coil embolization of the bleeding right upper polar segmental artery was done. After stabilization, MTP was done at 12th week of gestation. Counselling and consent for continuing or aborting the pregnancy is of utmost importance for best possible outcome for patient and foetus.

摘要

血管平滑肌脂肪瘤(AML)是一种罕见的肾脏良性肿瘤,在孕期由于激素刺激会迅速生长,导致破裂。多数报道的破裂性AML发生在孕晚期。我们报告一例妊娠10周时发生破裂的血管平滑肌脂肪瘤,这是单胎妊娠中已知最早的破裂病例。该AML在孕期形成假性动脉瘤并发生瘤外破裂,这一发现尚未见文献报道。在保守治疗的最初两天,患者有活动性出血且肾周血肿不断扩大。因此,在进行咨询并获得终止妊娠(MTP)的事先知情书面同意后,先进行了腹部计算机断层扫描及血管造影,随后对出血的右上极节段动脉进行了紧急线圈栓塞。病情稳定后,在妊娠12周时进行了MTP。对于患者和胎儿获得最佳可能结局而言,就继续妊娠还是终止妊娠进行咨询并取得同意至关重要。

相似文献

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Angiomyolipoma with vascular invasion during pregnancy.妊娠期间伴血管侵犯的血管平滑肌脂肪瘤
Ann Vasc Surg. 2011 Nov;25(8):1138.e9-13. doi: 10.1016/j.avsg.2011.05.023.

本文引用的文献

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Renal angiomyolipomas--a study of 18 cases.
Indian J Pathol Microbiol. 2005 Oct;48(4):459-63.
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[Influence of pregnancy on renal angiomyolipoma].[妊娠对肾血管平滑肌脂肪瘤的影响]
Gynecol Obstet Fertil. 2005 Nov;33(11):898-906. doi: 10.1016/j.gyobfe.2005.09.015. Epub 2005 Oct 26.

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