Del Sal Alice, Haumont Edouard, Pigeolet Manon, Gaume Mathilde, Riouallon Guillaume, Bahi Buisson Nadia, Linglart Agnes, Desguerre Isabelle, Pannier Stephanie, Miladi Lotfi
Department of Pediatric Orthopedic Surgery, Hôpital Universitaire Necker-Enfants Malades, Paris Cité University, 75015 Paris, France.
Faculty of Medicine, Université Libre de Bruxelles, 1050 Brussels, Belgium.
J Clin Med. 2025 Jan 27;14(3):849. doi: 10.3390/jcm14030849.
: This is a retrospective study. The aim of this study is to report the results of bipolar minimally invasive fusionless surgery for scoliosis in Rett syndrome with a minimum follow-up of 2 years. Conservative treatment is often not effective in Rett syndrome scoliosis. Posterior spinal fusion (PSF) has a high rate of complications; early surgery using traditional growing rods (TGRs) controls the deformity while preserving spinal and thoracic growth before arthrodesis. The need for surgical rod lengthening still has a high rate of complications and costs. : We recorded the clinical and radiological outcomes of 22 consecutive patients with Rett scoliosis who underwent bipolar fusionless surgery with a mean follow-up of 56 months (24-99). We performed a bilateral construct with rods (with or without a self-sliding device) anchored proximally with four hook claws distally to the pelvis by ilio-sacral (IS) screws through a minimally invasive approach. : The Cobb angle was reduced from 74.4° initially to 28.9° postoperatively and to 25.7° at the last follow-up, which corresponds to a 65% correction of the initial deformity. The gain was maintained at the last follow-up. None of the patients required spinal fusion at skeletal maturity (55% of our patients reached skeletal maturity). There was a gain in body weight (27.97 kg at preoperative time and 33.04 kg at postoperative time). The surgical complication rate was 32%. : We recorded the stable correction of deformities and weight gain over time using the bipolar minimally invasive fusionless technique with a reduced rate of complication compared to arthrodesis. The arthrodesis was not necessary at skeletal maturity, thanks to the delayed natural ankylosis of a fixed spine.
这是一项回顾性研究。本研究的目的是报告雷特综合征脊柱侧弯的双极微创无融合手术结果,随访时间至少为2年。保守治疗对雷特综合征脊柱侧弯通常无效。后路脊柱融合术(PSF)并发症发生率高;早期使用传统生长棒(TGRs)手术在融合前可控制畸形,同时保留脊柱和胸廓生长。手术延长棒的需求仍有较高的并发症发生率和成本。
我们记录了22例连续接受双极无融合手术的雷特脊柱侧弯患者的临床和放射学结果,平均随访56个月(24 - 99个月)。我们采用微创方法,通过双侧植入带棒结构(有或无自滑动装置),近端用四个钩爪固定,远端通过髂骶(IS)螺钉固定于骨盆。
Cobb角从最初的74.4°降至术后的28.9°,末次随访时为25.7°,相当于初始畸形矫正了65%。末次随访时矫正效果得以维持。没有患者在骨骼成熟时需要脊柱融合(我们55%的患者达到了骨骼成熟)。体重有所增加(术前体重27.97 kg,术后体重33.04 kg)。手术并发症发生率为32%。
我们记录了使用双极微创无融合技术随着时间推移畸形的稳定矫正和体重增加,与融合术相比并发症发生率降低。由于固定脊柱的自然延迟融合,骨骼成熟时无需进行融合术。