Kim Seong Gwang, Choi Hye Jeong, Cho Kyung Gi, Kim Jung Youn, Kim Sang Heum
J Korean Soc Radiol. 2025 Jan;86(1):185-190. doi: 10.3348/jksr.2024.0088. Epub 2025 Jan 20.
Multiple cranial neuropathies are complex neurological disorders that present significant treatment challenges due to their intricate and multifaceted underlying causes. Persistent trigeminal artery variant (PTAV) is an unusual anastomosis that connects the internal carotid artery to the cerebellar artery, bypassing the basilar artery. The incidence of PTAVs is approximately 0.18% and neurovascular compression is rarely reported. Patients with schwannomatosis typically have multiple schwannomas without vestibular nerve involvement, which may develop in the spinal nerve roots and, less commonly, in the cranial nerves. We report the case of a 53-year-old female with trigeminal neuralgia associated with PTAV and schwannomatosis in the abducens and lower cranial nerves as dual etiologies for multiple cranial neuropathies.
多发性颅神经病变是复杂的神经系统疾病，由于其潜在病因复杂且多方面，带来了重大的治疗挑战。持续性三叉动脉变异（PTAV）是一种不寻常的吻合，它将颈内动脉与小脑动脉相连，绕过基底动脉。PTAV的发生率约为0.18%，神经血管受压的情况很少有报道。神经鞘瘤病患者通常有多个神经鞘瘤，不累及前庭神经，这些神经鞘瘤可能发生在脊神经根，较少发生在颅神经。我们报告了一例53岁女性病例，其患有三叉神经痛，同时伴有PTAV以及展神经和低位颅神经的神经鞘瘤病，这两种情况作为多发性颅神经病变的双重病因。
