Deng Dongzhou, Hu Ying, Bing Dan
Department of Otolaryngology Head and Neck Surgery,Tongji Hospital,Tongji Medical College,Huazhong University of Science and Technology,Wuhan,430030,China.
Department of Radiology,Tongji Hospital,Tongji Medical College,Huazhong University of Science and Technology.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2025 Mar;39(3):255-259. doi: 10.13201/j.issn.2096-7993.2025.03.013.
This report describes a case of adult temporal bone Langerhans cell histiocytosis(LCH) that presented as posterior canal dehiscence syndrome(PCDS). The patient initially presented with vertigo, tinnitus, and hearing loss. Computed tomography(CT) revealed erosive changes in the mastoid and posterior semicircular canal. After the operation, the patient's hearing and vestibular symptoms disappeared and postoperative recovery was favorable. Adult LCH is relatively rare, and this case serves as an example to discuss the clinical features and treatment options of this disease, followed by a literature review.
本报告描述了一例表现为后半规管裂综合征(PCDS)的成人颞骨朗格汉斯细胞组织细胞增多症(LCH)。患者最初表现为眩晕、耳鸣和听力损失。计算机断层扫描(CT)显示乳突和后半规管有侵蚀性改变。手术后,患者的听力和前庭症状消失,术后恢复良好。成人LCH相对罕见,本病例作为一个例子来讨论该疾病的临床特征和治疗选择,随后进行文献综述。