Tsuchiya M, Oshio C, Asakura H, Ishii H, Aoki I, Miyairi M
Department of Internal Medicine, School of Medicine, Keio University, Tokyo, Japan.
Gastroenterology. 1978 Jul;75(1):114-7.
Budd-Chiari syndrome associated with protein-losing enteropathy is reported. A 26-year-old male suffered from ascites, edema in the lower extremities, and engorgement of ascending veins on the abdominal wall. The diagnosis of Budd-Chiari syndrome was made by inferior vena cavography. The 131I-polyvinylpyrrolidone test showed the association of protein-losing enteropathy. The surgical operation was performed successfully, resulting in a marked improvement of signs and symptoms. To date, no similar case has yet been reported. There are, however, a number of reported cases of hypoproteinemia in Budd-Chiari syndrome, which might have been associated with a protein-losing enteropathy.
报告了一例与蛋白丢失性肠病相关的布加综合征。一名26岁男性患者出现腹水、下肢水肿和腹壁上行静脉充盈。通过下腔静脉造影诊断为布加综合征。131I-聚乙烯吡咯烷酮试验显示存在蛋白丢失性肠病。手术成功进行，体征和症状明显改善。迄今为止，尚未有类似病例报道。然而，有许多关于布加综合征患者低蛋白血症的报道病例，这些病例可能与蛋白丢失性肠病有关。
