一例罕见的无内脏异位综合征的下腔静脉中断合并肺动脉瓣狭窄病例。
A rare case of inferior vena cava interruption and pulmonary valve stenosis in the absence of heterotaxy syndrome.
作者信息
Rajab Tuqa, Abou Nukta Moayad, Bannoud Nour, Haddad Sultaneh, Aljarmakani Dimah, Ali Doaa Mukhtar Mohammed, Jama Amal Mohamed H Hassan, Srour Samir
机构信息
Faculty of Medicine, Tartous University, Tartous, Syrian Arab Republic.
Faculty of Medicine, Damascus University, Damascus, Syrian Arab Republic.
出版信息
Ann Med Surg (Lond). 2025 Jan 21;87(2):964-967. doi: 10.1097/MS9.0000000000002906. eCollection 2025 Feb.
INTRODUCTION
The complete absence hepatic portion of the inferior vena cava (IVC) is known as "interruption" of the IVC. Congenital interruption of the IVC can rarely occur in patients with a normal visceroatrial situs.
CASE PRESENTATION
We present a case of an 8-year-old male child who exhibited mild dyspnea. Further evaluation revealed an interruption of the IVC and pulmonary valve stenosis, without heterotaxy.
DISCUSSION
It is important to recognize that interruption of the IVC can occur independently or as part of a syndrome. Therefore, thorough investigations should be conducted for each patient.
CONCLUSION
More research is needed to explore the associations between IVC interruption and pulmonary valve stenosis.
引言
下腔静脉（IVC）肝段完全缺如被称为IVC“中断”。先天性IVC中断在脏器心房位置正常的患者中很少见。
病例报告
我们报告一例8岁男性儿童，表现为轻度呼吸困难。进一步评估发现IVC中断和肺动脉瓣狭窄，无内脏异位。
讨论
重要的是要认识到IVC中断可单独发生或作为综合征的一部分出现。因此，应对每位患者进行全面检查。
结论
需要更多研究来探索IVC中断与肺动脉瓣狭窄之间的关联。
Zotero 插件