Kaveggia F F
Am J Med Genet. 1985 Jun;21(2):213-23. doi: 10.1002/ajmg.1320210203.
Life-table analyses were performed on 1,915 severely/profoundly retarded institutionalized persons. Data on probability of death and hazard rates are presented according to sex and previously described diagnostic/etiologic categories. The median remaining lifetime for a resident of Central Wisconsin Center on admission was found to be greater than 25 years. The average age of admission was 7.3 years with a range of 0-66 years. The highest death rate was noted in residents with inborn errors of metabolism; the lowest death rate was in residents with primary seizures disorders. On admission, the median remaining lifetime was 8.81 +/- 4.16 years (95% confidence interval) for residents with inborn errors of metabolism, 18.56 +/- 4.26 years for residents with primary CNS malformations, and 24.66 +/- 4.05 years for residents with known syndromes. Residents of all other diagnostic/etiologic categories had a median remaining lifetime of greater than 25 years.
对1915名重度/极重度智力发育迟缓的机构收容人员进行了寿命表分析。根据性别以及先前描述的诊断/病因类别，给出了死亡概率和风险率的数据。发现威斯康星州中部中心的住院患者入院时的剩余寿命中位数超过25年。入院的平均年龄为7.3岁，范围在0至66岁之间。代谢先天性缺陷患者的死亡率最高；原发性癫痫疾病患者的死亡率最低。入院时，代谢先天性缺陷患者的剩余寿命中位数为8.81±4.16年（95%置信区间），原发性中枢神经系统畸形患者为18.56±4.26年，已知综合征患者为24.66±4.05年。所有其他诊断/病因类别的住院患者剩余寿命中位数均超过25年。
