通过全面的以患者为中心的护理优化胱氨酸病的长期治疗效果。 - Suppr

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超能文献

Optimizing Long-Term Outcomes in Cystinosis With Comprehensive Patient-Centered Care.

作者信息

Elenberg Ewa

机构信息

Texas Children's Hospital and Baylor College of Medicine, Houston, Texas, USA.

出版信息

Kidney Int Rep. 2025 Mar 4;10(3 Suppl):S775-S778. doi: 10.1016/j.ekir.2024.10.038. eCollection 2025 Mar.

DOI:10.1016/j.ekir.2024.10.038

PMID:40143950

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11935153/

Abstract

摘要

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9be/11935153/ac3458e7d60b/gr1.jpg

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Pediatr Nephrol. 2024 Aug;39(8):2283-2292. doi: 10.1007/s00467-023-06225-0. Epub 2023 Dec 21.

Beneficial effects of starting oral cysteamine treatment in the first 2 months of life on glomerular and tubular kidney function in infantile nephropathic cystinosis.胱胺治疗在生命的头 2 个月开始对婴儿胱氨酸病的肾小球和肾小管肾脏功能的有益影响。

Mol Genet Metab. 2022 Aug;136(4):282-288. doi: 10.1016/j.ymgme.2022.06.009. Epub 2022 Jul 1.

Adult complications of nephropathic cystinosis: a systematic review.肾性胱氨酸病的成人并发症：一项系统评价。

Pediatr Nephrol. 2021 Feb;36(2):223-236. doi: 10.1007/s00467-020-04487-6. Epub 2020 Feb 3.

Effects of long-term cysteamine treatment in patients with cystinosis.胱氨酸病患者长期半胱胺治疗的效果。

Pediatr Nephrol. 2019 Apr;34(4):571-578. doi: 10.1007/s00467-017-3856-4. Epub 2017 Dec 19.

Controversies and research agenda in nephropathic cystinosis: conclusions from a "Kidney Disease: Improving Global Outcomes" (KDIGO) Controversies Conference.肾性胱氨酸病的争议和研究议程：“改善全球肾脏病预后组织”（KDIGO）争议会议的结论。

Kidney Int. 2016 Jun;89(6):1192-203. doi: 10.1016/j.kint.2016.01.033.

Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults.半胱氨酸治疗可延缓晚期青少年和成年患者的囊纤维化肾病进展。

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Ann Intern Med. 2007 Aug 21;147(4):242-50. doi: 10.7326/0003-4819-147-4-200708210-00006.

Cystinosis.胱氨酸病

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