Kondo Yuki, Matsugi Akiyoshi, Bando Kyota, Kikuchi Yutaka, Maruyama Hiromi, Miyazaki Yuta, Hara Takatoshi, Takahashi Yuji, Mizusawa Hidehiro
Department of Physical Rehabilitation, National Center of Neurology and Psychiatry, National Center Hospital, 4-1-1 Ogawa-higashi-cho, Kodaira-shi, Tokyo, 187-8551, Japan.
Faculty of Rehabilitation, Shijonawate Gakuen University, 5-11-10, Hojo, Daito-Shi, 574-0011, Osaka, Japan.
Cerebellum. 2025 Apr 1;24(3):78. doi: 10.1007/s12311-025-01831-0.
Patients with spinocerebellar degeneration (SCD) and multiple system atrophy (MSA) encounter various challenges in daily life due to ataxia and other symptoms. A comprehensive understanding of their diverse needs can improve the effectiveness of rehabilitation interventions.
This study aims to identify the daily challenges faced by patients with SCD and MSA in Japan, focusing on differences between ambulatory and non-ambulatory patients.
A postal survey was conducted from March to May 2023, targeting members of the Japanese Society of Ataxia Patients diagnosed with SCD and MSA. The questionnaire assessed respondent demographics and symptoms impacting daily life.
From the 283 responses received, 152 were deemed valid for analysis. Non-ambulatory patients reported significantly more difficulties across multiple items in the activities domain. Furthermore, subjective unsteadiness, difficulty speaking, and increased fall risk were identified as having the most significant impact on daily life, regardless of walking ability.
These findings highlight the need to adapt rehabilitation approaches for patients with SCD and MSA as their disease progresses, emphasizing comprehensive assessment methods and multidisciplinary care to enhance their quality of life.
脊髓小脑变性（SCD）和多系统萎缩（MSA）患者由于共济失调和其他症状，在日常生活中面临各种挑战。全面了解他们的多样化需求可以提高康复干预的效果。
本研究旨在确定日本SCD和MSA患者在日常生活中面临的挑战，重点关注能行走和不能行走患者之间的差异。
2023年3月至5月进行了一项邮寄调查，目标是被诊断为SCD和MSA的日本共济失调患者协会成员。问卷评估了受访者的人口统计学特征和影响日常生活的症状。
在收到的283份回复中，152份被认为可用于分析。不能行走的患者在活动领域的多个项目中报告的困难明显更多。此外，无论行走能力如何，主观不稳定、说话困难和跌倒风险增加被确定为对日常生活影响最大的因素。
这些发现凸显了随着SCD和MSA患者病情进展调整康复方法的必要性，强调综合评估方法和多学科护理以提高他们的生活质量。
