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左束支起搏改善终末期肥厚型心肌病预后:一例报告

Left Bundle Branch Pacing Improved the Outcome of End-Stage Hypertrophic Cardiomyopathy: A Case Report.

作者信息

Lin Manxin, Huang Shufen, Huang Xinyi, Li Linlin, Cai Binni

机构信息

Division of Cardiology, Xiamen Cardiovascular Hospital, Xiamen University, Xiamen, Fujian, China.

Division of Echocardiography, Xiamen Cardiovascular Hospital, Xiamen University, Xiamen, Fujian, China.

出版信息

Ann Noninvasive Electrocardiol. 2025 May;30(3):e70073. doi: 10.1111/anec.70073.

Abstract

Patients with hypertrophic cardiomyopathy (HCM) enter the terminal stage when developed left ventricle enlargement and ejection fraction (EF) reduction. The concomitant complete left bundle branch block (LBBB) is considered an important factor related to poor outcome. Previous research suggested that biventricular pacing has limited effects on such patients. We report a case with end-stage hypertrophic cardiomyopathy who had a miraculous recovery after receiving successful left bundle branch pacing (LBBP).

摘要

肥厚型心肌病(HCM)患者出现左心室扩大和射血分数(EF)降低时进入终末期。合并的完全性左束支传导阻滞(LBBB)被认为是与不良预后相关的重要因素。既往研究表明双心室起搏对此类患者效果有限。我们报告1例终末期肥厚型心肌病患者,在成功接受左束支起搏(LBBP)后奇迹般康复。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/70e3/11969566/5097c58d60a9/ANEC-30-e70073-g004.jpg

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