Fakhri A, Fishman E K, Jones B, Kuhajda F, Siegelman S S
J Comput Assist Tomogr. 1985 Jul-Aug;9(4):767-70.
We present two patients with biopsy proven primary intestinal lymphangiectasia in whom CT demonstrated diffuse nodular thickening of small bowel without adenopathy or hepatosplenomegaly. One patient had extensive ascites. Although the CT findings are not specific to lymphangiectasia, they may allow one to suggest the diagnosis in the patient with protein losing enteropathy and help distinguish it from inflammatory bowel disease, lymphoma, celiac disease, or Whipple disease.
我们报告了两名经活检证实为原发性小肠淋巴管扩张症的患者，其CT显示小肠弥漫性结节状增厚，无淋巴结肿大或肝脾肿大。其中一名患者有大量腹水。虽然CT表现并非淋巴管扩张症所特有，但对于患有蛋白丢失性肠病的患者，这些表现可能有助于提示诊断，并有助于将其与炎症性肠病、淋巴瘤、乳糜泻或惠普尔病相鉴别。
