Griffin J D, Spriggs D, Wisch J S, Kufe D W
J Clin Oncol. 1985 Jul;3(7):982-91. doi: 10.1200/JCO.1985.3.7.982.
Preleukemic syndromes compose a group of acquired bone marrow disorders characterized by dysplastic maturation of hematopoietic cells and peripheral blood cytopenias. These syndromes have been generally considered untreatable. We administered low doses of cytosine arabinoside by continuous infusion for 14 to 21 days (20 mg/m2/d) to 16 patients with preleukemia in various stages of evolution to acute leukemia. Steady state plasma cytosine arabinoside levels ranged from 41.8 to 64.2 nmol/L. Eleven patients demonstrated marked improvement in hematopoiesis and loss of transfusion requirements for periods ranging from two to 27 + months. All but one responding patient developed recurrent pancytopenia, but additional responses to low-dose cytosine arabinoside were achieved in five of five retreated patients. Median overall survival time is 12 months for the 11 responding cases, and nine months for nonresponders. The major toxicity of low-dose cytosine arabinoside is myelosuppression, and most patients required platelet transfusion support and administration of antibiotics. Chromosome analyses demonstrated evolution to a new clone of hematopoietic cells in three patients, and persistence of the same abnormal clone in another patient. These results suggest that low-dose cytosine arabinoside therapy may result in improved hematopoiesis by promoting maturation or by selecting new stem cell clones. Low-dose cytosine arabinoside therapy thus deserves further evaluation both as a single agent and in combination with other agents in the treatment of myelodysplastic syndromes.
白血病前期综合征是一组获得性骨髓疾病,其特征为造血细胞发育异常成熟和外周血细胞减少。这些综合征通常被认为无法治疗。我们对16例处于急性白血病演变不同阶段的白血病前期患者连续输注低剂量阿糖胞苷14至21天(20mg/m²/天)。稳态血浆阿糖胞苷水平在41.8至64.2nmol/L之间。11例患者的造血功能有显著改善,在2至27个多月的时间内不再需要输血。除1例有反应的患者外,所有患者均出现复发性全血细胞减少,但5例再次接受治疗的患者中有5例对低剂量阿糖胞苷再次产生反应。11例有反应病例的中位总生存时间为12个月,无反应者为9个月。低剂量阿糖胞苷的主要毒性是骨髓抑制,大多数患者需要血小板输注支持和使用抗生素。染色体分析显示,3例患者造血细胞演变为新的克隆,另1例患者同一异常克隆持续存在。这些结果表明,低剂量阿糖胞苷治疗可能通过促进成熟或选择新的干细胞克隆来改善造血功能。因此,低剂量阿糖胞苷治疗作为单一药物或与其他药物联合治疗骨髓增生异常综合征值得进一步评估。