Mathew Priya, Singh Aditya Pratap, Mittal Priyanka, Mathur Praveen
Department of Pediatric Surgery, Sawai Man Singh Medical College, Jaipur, Rajasthan, India.
Int J Trichology. 2024 Jan-Dec;16(1-6):42-44. doi: 10.4103/ijt.ijt_70_21. Epub 2025 Apr 18.
Rapunzel syndrome (RS) can have a varied clinical presentation, spanning from being asymptomatic to having a fatal outcome. If left untreated, complications are inevitable. This case highlights an amalgamation of varied presentations of RS with a daughter bezoar acting as a lead point for intussusception, its management, and favorable result. The purpose of this discussion is to throw the focus on the blend of diverse clinical findings and complications of RS with a daughter bezoar; and the importance of early surgical intervention followed by psychological support and psychiatric treatment, as a key to a successful outcome.
长发公主综合征(RS)的临床表现多样,从无症状到出现致命后果不等。若不治疗,并发症不可避免。本病例突出了RS多种表现形式与作为肠套叠起始点的胃石合并出现的情况、其治疗及良好结果。本次讨论的目的是聚焦RS的各种临床发现及并发症与胃石的混合情况;以及早期手术干预并随后给予心理支持和精神治疗作为取得成功结果关键的重要性。