Akor Francis, Thenat Toby, Hussain Sajjad, Kumar Suresh
Department of Paediatrics, Darent Valley Hospital Dartford, Kent, United Kingdom.
Niger Med J. 2025 Apr 3;66(1):379-384. doi: 10.71480/nmj.v66i1.615. eCollection 2025 Jan-Feb.
Sickle cell disease is an inherited disorder of haemoglobin formation, predominantly affecting individuals of African, Indian, or Mediterranean descent. Acute painful episodes frequently occur in these patients due to the blockage of small blood vessels by sickled cells, leading to tissue infarction. Two children of Nigerian descent, presented with severe headaches during a painful crisis episode with associated swelling on their scalps. CT imaging in both cases showed subgaleal haematoma which was managed conservatively in addition to managing the painful crisis with a good outcome. This report highlights the clinical presentation, diagnostic approach, and management of this uncommon complication of sickle cell anaemia.
镰状细胞病是一种血红蛋白形成的遗传性疾病,主要影响非洲、印度或地中海血统的个体。由于镰状细胞阻塞小血管,导致组织梗死,这些患者经常发生急性疼痛发作。两名尼日利亚血统的儿童在疼痛危象发作期间出现严重头痛,并伴有头皮肿胀。两例患者的CT成像均显示帽状腱膜下血肿,除了对疼痛危象进行治疗外,对血肿进行了保守处理,效果良好。本报告强调了镰状细胞贫血这种罕见并发症的临床表现、诊断方法和治疗。