Gu Mi-Jin
Department of Pathology, Yeungnam University College of Medicine, 170 Hyeonchung-ro, Nam-gu, Daegu 42415, Republic of Korea.
J Surg Case Rep. 2025 Apr 30;2025(5):rjaf261. doi: 10.1093/jscr/rjaf261. eCollection 2025 May.
Primary retroperitoneal mucinous cystic tumor (PRMCT) is rare and preoperative diagnosis is challenging due to their rarity, lack of specific diagnostic imaging, clinical presentation, and tumor markers. We present an extremely rare case of PRMCT of borderline malignancy and summarize the characteristics of previously reported cases. Although the prognosis and optimal therapeutic strategies require further investigation due to its rarity, we should be considered when dealing with retroperitoneal cystic lesions.
原发性腹膜后黏液性囊性肿瘤(PRMCT)较为罕见,由于其罕见性、缺乏特异性诊断影像学表现、临床表现及肿瘤标志物,术前诊断具有挑战性。我们报告一例极其罕见的交界性恶性PRMCT病例,并总结既往报道病例的特征。尽管因其罕见性,其预后及最佳治疗策略仍需进一步研究,但在处理腹膜后囊性病变时应予以考虑。