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一例罕见的巨大心包黏液纤维肉瘤病例。

An exceptional case of huge myxofibrosarcoma of the pericardium.

作者信息

Laaroussi Mehdi, Tribak Mohammed, Idrissa Abdel Malick, Maiga Abdramane, Boite Adama, Jihad Briki, Benlafqih Chakib, Sayah Rochde, Cherti Mohamed, Laaroussi Mohammed

机构信息

Cardiology "B" Department, Ibn Sina University and Hospital Centre, Mohammed V Souissi University, Rabat 10800, Morocco.

Cardiovascular Surgery "A" Department, Ibn Sina University and Hospital Centre, Mohammed V Souissi University, Rabat 10800, Morocco.

出版信息

J Surg Case Rep. 2025 May 2;2025(5):rjaf270. doi: 10.1093/jscr/rjaf270. eCollection 2025 May.

Abstract

Primary cardiac myxofibrosarcoma is a rare malignant tumour usually found in the left atrium. Its pericardial location is extremely rare, and its management is mainly based on surgery. We report a historical case of myxofibrosarcoma of the pericardium weighing 4200 g.

摘要

原发性心脏黏液纤维肉瘤是一种罕见的恶性肿瘤,通常发生于左心房。其位于心包的情况极为罕见,治疗主要基于手术。我们报告一例心包黏液纤维肉瘤病例,肿瘤重达4200克。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/70ac/12045935/f31eecf7907e/rjaf270f1.jpg

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