Hill D J, Martin A J, Davidson G P, Smith G S
Med J Aust. 1985 Sep 16;143(6):230-2. doi: 10.5694/j.1326-5377.1985.tb122953.x.
Life tables were calculated for 205 South Australians with cystic fibrosis. An improvement in survival was noted between 1948 and 1982. Ninety-three per cent of patients who were diagnosed as having cystic fibrosis after 1973 were alive at 14 years of age, compared with 40% of those who were diagnosed between 1948 and 1973. A Cystic Fibrosis Clinic was established in 1973 and much of this improvement is attributed to the care provided by this centre. Deaths from meconium ileus fell from 58% of infants with this complication between 1948 and 1973 to only 8% between 1973 and 1983, in spite of the increasing incidence of patients who were chronically colonized with Pseudomonas aeruginosa (currently 68% of patients). These figures are similar to those from Victoria and from other cystic fibrosis centres in North America. The improvement in survival means that adults now comprise a quarter of the patients with cystic fibrosis in South Australia, and that adult institutions need to be aware of these patients and their needs.
为205名患有囊性纤维化的南澳大利亚人计算了生命表。结果显示1948年至1982年间生存率有所提高。1973年后被诊断为患有囊性纤维化的患者中，93%在14岁时仍存活，而1948年至1973年间被诊断出的患者这一比例为40%。1973年设立了囊性纤维化诊所，生存率的提高在很大程度上归功于该中心提供的护理。尽管长期感染铜绿假单胞菌的患者比例不断增加（目前为68%），但胎粪性肠梗阻导致的死亡比例从1948年至1973年间患有该并发症婴儿的58%降至1973年至1983年间的仅8%。这些数据与来自维多利亚州以及北美的其他囊性纤维化中心的数据相似。生存率的提高意味着成年人现在占南澳大利亚囊性纤维化患者的四分之一，成人医疗机构需要了解这些患者及其需求。
