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一种罕见的眶上嵴肿物:伴有脂肪细胞化生的软骨样汗管瘤。

A Rare Supraorbital Ridge Mass: The Chondroid Syringoma with Adipocytic Metaplasia.

作者信息

Prasad Anil, Kumar Binod, Mehta Sameer Kumar, Mishra Minakshi

机构信息

Department of Pathology, Tata Main Hospital, Jamshedpur, Jharkhand, India.

Department of Dermatology, Tata Main Hospital, Jamshedpur, Jharkhand, India.

出版信息

Int J Appl Basic Med Res. 2025 Jan-Mar;15(1):60-62. doi: 10.4103/ijabmr.ijabmr_363_24. Epub 2025 Jan 9.

DOI:10.4103/ijabmr.ijabmr_363_24
PMID:40336764
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12054656/
Abstract

Chondroid syringoma (CS) is a rare benign skin adnexal neoplasm. Its incidence is very low among all primary skin tumors. Diagnosing it clinically can be difficult as it closely resembles other benign salivary or adnexal neoplasms. Until now, only a few cases have been reported from the periorbital region. Clinically, it can be mistaken for epidermal cysts, but ectopic salivary glands are a close differential diagnosis. To diagnose it, a complete removal is usually required, followed by a histopathological examination. We present a unique case of a 45-year-old female patient with a CS in her right supraorbital ridge and review the pertinent literature.

摘要

软骨样汗腺腺瘤(CS)是一种罕见的皮肤附属器良性肿瘤。在所有原发性皮肤肿瘤中,其发病率极低。临床上诊断该病可能较为困难,因为它与其他良性涎腺或附属器肿瘤极为相似。迄今为止,仅少数眶周区域病例有报道。临床上,它可能被误诊为表皮样囊肿,但异位涎腺是相近的鉴别诊断对象。要诊断该病,通常需要完整切除,随后进行组织病理学检查。我们报告一例45岁女性患者右眶上嵴软骨样汗腺腺瘤的独特病例,并复习相关文献。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/b86fb59ad547/IJABMR-15-60-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/8dfdc63a2473/IJABMR-15-60-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/36c3f150e83a/IJABMR-15-60-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/b86fb59ad547/IJABMR-15-60-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/8dfdc63a2473/IJABMR-15-60-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/36c3f150e83a/IJABMR-15-60-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad6b/12054656/b86fb59ad547/IJABMR-15-60-g003.jpg

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Int J Appl Basic Med Res. 2025 Jan-Mar;15(1):60-62. doi: 10.4103/ijabmr.ijabmr_363_24. Epub 2025 Jan 9.
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本文引用的文献

1
Benign chondroid syringoma affecting the upper lip: Report of a rare case and review of literature.发生于上唇的良性软骨样汗腺腺瘤:1例罕见病例报告及文献复习
J Oral Maxillofac Pathol. 2018 Sep-Dec;22(3):401-405. doi: 10.4103/jomfp.JOMFP_35_18.
2
A Case of a Malignant Cutaneous Mixed Tumor (Chondroid Syringoma) of the Scapula Treated With Staged Margin-Controlled Excision.1例采用分期切缘控制切除治疗的肩胛骨恶性皮肤混合瘤(软骨样汗腺腺瘤)
Am J Dermatopathol. 2018 Sep;40(9):679-681. doi: 10.1097/DAD.0000000000001131.
3
Chondroid Syringoma on Face.
面部软骨样汗腺螺旋瘤
Arch Craniofac Surg. 2016 Sep;17(3):173-175. doi: 10.7181/acfs.2016.17.3.173. Epub 2016 Sep 23.
4
Chondroid syringoma of the medial canthus.内眦部软骨样汗腺螺旋瘤
Case Rep Otolaryngol. 2014;2014:158527. doi: 10.1155/2014/158527. Epub 2014 Mar 11.
5
Chondroid syringoma. Mixed tumor of skin, salivary gland type.软骨样汗腺腺瘤。皮肤混合瘤,涎腺型。
Arch Dermatol. 1961 Nov;84:835-47. doi: 10.1001/archderm.1961.01580170129018.
6
Myoepithelial tumors of soft tissue: a clinicopathologic and immunohistochemical study of 101 cases with evaluation of prognostic parameters.软组织肌上皮肿瘤:101例临床病理及免疫组化研究并评估预后参数
Am J Surg Pathol. 2003 Sep;27(9):1183-96. doi: 10.1097/00000478-200309000-00001.
7
Chondroid syringoma: a diagnosis more frequent than expected.软骨样汗腺螺旋瘤:一种比预期更常见的诊断。
Dermatol Surg. 2003 Feb;29(2):179-81. doi: 10.1046/j.1524-4725.2003.29045.x.
8
Recurrent malignant chondroid syringoma of the foot: a case report and review of the literature.足部复发性恶性软骨样汗腺腺瘤:一例报告并文献复习
Am J Clin Oncol. 2000 Jun;23(3):227-32. doi: 10.1097/00000421-200006000-00003.