Seki Koichiro, Yamamoto Reiko, Yoshinaga Koichi, Takeuchi Mamoru
Anesthesiology and Critical Care Medicine, Jichi Medical University, Shimotsuke, JPN.
Cureus. 2025 May 3;17(5):e83435. doi: 10.7759/cureus.83435. eCollection 2025 May.
Intravenous leiomyomatosis (IVL) with intracardiac extension can cause circulatory collapse during anesthetic induction due to right heart obstruction. We report the case of a 63-year-old woman with IVL extending into the right ventricle, presenting with right heart failure and shock. To maintain hemodynamic stability and facilitate tumor resection, we established cardiopulmonary bypass (CPB) under local anesthesia before inducing general anesthesia. Preoperative imaging revealed a tumor extending from the right ovarian vein to the right ventricle, causing circulatory failure. In the operating room, CPB was initiated via femoral cannulation under local anesthesia with analgosedation to maintain spontaneous breathing, followed by general anesthesia induction. A median sternotomy was performed, and an additional venous cannula was placed in the superior vena cava to achieve total CPB. The tumor was resected from the right heart and inferior vena cava. The patient was weaned from CPB and ventilation without complications. Pathology was later confirmed to be IVL. She was discharged on postoperative day 30. Establishing CPB before anesthetic induction maintained hemodynamic stability in this patient with IVL, intracardiac extension, and right heart failure, allowing for safe tumor resection.
伴有心内扩展的静脉内平滑肌瘤病(IVL)在麻醉诱导期间可因右心梗阻导致循环衰竭。我们报告一例63岁女性,其IVL延伸至右心室,表现为右心衰竭和休克。为维持血流动力学稳定并便于肿瘤切除,我们在诱导全身麻醉前于局部麻醉下建立了体外循环(CPB)。术前影像学检查显示肿瘤从右卵巢静脉延伸至右心室,导致循环衰竭。在手术室,于局部麻醉下经股动脉插管并给予镇痛镇静以维持自主呼吸后启动CPB,随后进行全身麻醉诱导。行正中胸骨切开术,并在上腔静脉置入另一根静脉插管以实现完全CPB。肿瘤从右心和下腔静脉切除。患者顺利脱离CPB和通气,未出现并发症。病理检查后来证实为IVL。她于术后第30天出院。在麻醉诱导前建立CPB维持了该患有IVL、心内扩展和右心衰竭患者的血流动力学稳定,从而得以安全地切除肿瘤。