Sfar Kaouthar, Jaheddine Fadwa, Maslouhi Kaoutar, Chait Fatima, Zhim Meriem, Kettani Najwa Ech-Cherif El, Fikri Meriem, Jiddane Mohamed, Touarsa Firdaous
Neuroradiology Department, Specialty Hospital of Rabat, Mohamed V University, Rabat, Morocco.
Radiol Case Rep. 2025 May 17;20(8):3851-3854. doi: 10.1016/j.radcr.2025.04.074. eCollection 2025 Aug.
Hypoglossal schwannoma (HS) is a rare, benign tumor arising from the myelin-producing Schwann cells of the twelfth cranial nerve. This tumor typically appears as solid mass, with cystic patterns being extremely rare. A. Kaye classified HS into 3 types based on their origin: type A, completely intracranial; type B, intracranial with extracranial extension via the hypoglossal canal, often referred to as "dumbbell-shaped"; and type C, arising solely from the extracranial portion of the XII nerve. Tongue deviation and hypotrophy are the most common symptoms. MRI is the gold standard for accurately characterizing the lesion's features and assessing its relationship with the surrounding structures, while high-resolution CT scan of the skull base is valuable for surgical planning. The treatment of hypoglossal schwannoma (HS) is surgical excision. Advances in microsurgical techniques, radiosurgery and neurophysiological monitoring have significantly reduced mortality and morbidity. Here, we report a case of cystic dumbbell-shaped hypoglossal schwannoma in a 71-year-old woman, aiming to emphasize the clinical and radiological characteristics of this rare entity.
舌下神经鞘瘤(HS)是一种罕见的良性肿瘤,起源于第十二对脑神经产生髓磷脂的施万细胞。这种肿瘤通常表现为实性肿块,囊性形态极为罕见。A. 凯伊根据其起源将HS分为3型:A型,完全位于颅内;B型,颅内部分经舌下神经管向颅外延伸,常被称为“哑铃形”;C型,仅起源于第十二对脑神经的颅外部分。舌偏斜和萎缩是最常见的症状。MRI是准确描述病变特征并评估其与周围结构关系的金标准,而高分辨率颅底CT扫描对手术规划很有价值。舌下神经鞘瘤(HS)的治疗方法是手术切除。显微外科技术、放射外科和神经生理监测的进展显著降低了死亡率和发病率。在此,我们报告一例71岁女性的囊性哑铃形舌下神经鞘瘤病例,旨在强调这种罕见实体的临床和放射学特征。