Forrai Zsolt, Bánfi-Bacsárdi Fanni, Pilecky Dávid, Gergely Tamás G, Hanuska Laura Fanni, Schäffer Pál Péter, Kazay Ádám, Vértes Vivien, Vámos Máté, Andréka Péter, Piróth Zsolt, Nyolczas Noémi, Muk Balázs
1 Gottsegen Gyögy Országos Kardiovaszkuláris Intézet, Felnőtt Kardiológiai Osztály Budapest, Haller u. 29., 1096 Magyarország.
2 Szegedi Tudományegyetem, Szent-Györgyi Albert Orvostudományi Kar, Klinikai Orvostudományi Doktori Iskola Szeged Magyarország.
Orv Hetil. 2025 Jun 22;166(25):970-981. doi: 10.1556/650.2025.33289.
Introduction: The 2023 European Society of Cardiology Cardiomyopathy Guidelines emphasize the crucial role of a multiparametric approach in diagnosing. During the diagnostic workup of hypertrophic cardiomyopathy, besides echocardiography and cardiac magnetic resonance, ECG plays an important role. Based on literature data, only 4–18% of patients with hypertrophic cardiomyopathy have normal ECG, however, ECG deviations are often non-specific. Objective: To evaluate the ECG characteristics in a hypertrophic cardiomyopathy patient cohort followed-up at the Heart Failure Outpatient Clinic of Gottsegen National Cardiovascular Center. Method: We retrospectively analyzed the data and the first ECGs registered of patients with hypertrophic cardiomyopathy, diagnosed by cardiac magnetic resonance and/or genetic testing, followed-up between 01. 11. 2023 and 30. 09. 2024 at our Heart Failure Outpatient Clinic. Results: Data from 72 patients were evaluated, male: 58%, age: 49 (34–62) years, left ventricular ejection fraction: 63 (47–72)%, NYHA functional class: 2 (1–2), ICD/CRT-D: 47%. Based on the left ventricular outflow tract obstruction of ≥30 mmHg, 31% of the patients belonged to hypertrophic obstructive cardiomyopathy subgroup. Based on the ECGs analyzed, atrial fibrillation occurred in 6%. Interatrial conduction disturbances affected 29% of the patients. Atrioventricular and intraventricular conduction disturbances occurred in 50% (AV block: 20% [grade I: 18%, grade II: 2%, grade III: 0%], right bundle branch block: 14%, left bundle branch block: 16%, left anterior hemiblock: 13%, left posterior hemiblock: 3%, non-specific intraventricular conduction disturbance: 8%). The sensitivity of the Cornell, Sokolow–Lyon, and Peguero–Lo Presti “high voltage” criteria were low (23–14–25%). Pathological Q wave occurred in 42% of the patients, QRS fragmentation in 43% and corrected QT interval prolongation in 44%. T wave inversion was present in 94%, significant ST elevation in 21%, ST depression in 48%, while only 3% of patients had negative ECG. The only difference between hypertrophic obstructive cardiomyopathy and non-obstructive hypertrophic cardiomyopathy patients was the fulfillment of the Cornell criterion (45% vs. 15%, p = 0.044). Conclusions: A multimodal approach is essential in the diagnosis of hypertrophic cardiomyopathy. Based on our results, hypertrophic cardiomyopathy is often associated with heterogeneous ECG abnormalities. However, the early recognition of the ECG variations may help in the further diagnostic steps, contributing to the initiation of disease-modifying treatment. Orv Hetil. 2025; 166(25): 970–981.
2023年欧洲心脏病学会心肌病指南强调多参数方法在诊断中的关键作用。在肥厚型心肌病的诊断检查过程中,除了超声心动图和心脏磁共振成像外,心电图也发挥着重要作用。根据文献数据,仅有4%-18%的肥厚型心肌病患者心电图正常,然而,心电图异常往往不具有特异性。目的:评估在戈特塞根国家心血管中心心力衰竭门诊随访的肥厚型心肌病患者队列的心电图特征。方法:我们回顾性分析了经心脏磁共振成像和/或基因检测确诊为肥厚型心肌病、于2023年11月1日至2024年9月30日在我们心力衰竭门诊随访患者的数据及首次记录的心电图。结果:评估了72例患者的数据,男性占58%,年龄为49(34-62)岁,左心室射血分数为63(47-72)%,纽约心脏协会功能分级为2(1-2)级,植入式心律转复除颤器/心脏再同步化治疗-除颤器(ICD/CRT-D)比例为47%。基于左心室流出道梗阻≥30 mmHg,31%的患者属于肥厚型梗阻性心肌病亚组。根据分析的心电图,6%的患者发生心房颤动。房间传导障碍影响29%的患者。房室和室内传导障碍发生率为50%(房室传导阻滞:20%[I度:18%,II度:2%,III度:0%],右束支传导阻滞:14%,左束支传导阻滞:16%,左前分支阻滞:13%,左后分支阻滞:3%,非特异性室内传导障碍:8%)。康奈尔、索科洛-里昂和佩格罗-洛普雷蒂“高电压”标准的敏感性较低(23%-14%-25%)。42%的患者出现病理性Q波,43%出现QRS波碎裂,44%出现校正QT间期延长。94%的患者出现T波倒置,21%出现显著ST段抬高,48%出现ST段压低,而仅有3%的患者心电图正常。肥厚型梗阻性心肌病和非梗阻性肥厚型心肌病患者之间的唯一差异在于康奈尔标准的满足情况(45%对15%,p = 0.044)。结论:多模式方法对肥厚型心肌病的诊断至关重要。根据我们的结果,肥厚型心肌病常伴有异质性心电图异常。然而早期识别心电图变化可能有助于进一步的诊断步骤,有助于启动疾病修饰治疗。《匈牙利医学周报》。2025年;166(25):970-981。