Bar Sudipta, Wilson Kenneth A, Hilsabeck Tyler A U, Alderfer Sydney, Dammer Eric B, Burton Jordan B, Shah Samah, Holtz Anja, Carrera Enrique M, Beck Jennifer N, Chen Jackson H, Kauwe Grant, Seifar Fatemeh, Shantaraman Ananth, Tracy Tara E, Seyfried Nicholas T, Schilling Birgit, Ellerby Lisa M, Kapahi Pankaj
Buck Institute for Research on Aging, Novato, CA, USA.
Emory Center for Neurodegenerative Disease, Emory University School of Medicine, Atlanta, GA, USA.
Nat Metab. 2025 Jun 30. doi: 10.1038/s42255-025-01314-w.
Tauopathies encompass a range of neurodegenerative disorders, such as Alzheimer's disease (AD) and frontotemporal lobar degeneration with tau inclusions (FTLD-tau), for which there are currently no successful treatments. Here, we show impaired glycogen metabolism in the brain of a tauopathy Drosophila melanogaster model and people with AD, indicating a link between tauopathies and glycogen metabolism. We demonstrate that the breakdown of neuronal glycogen ameliorates the tauopathy phenotypes in flies and induced pluripotent stem cell (iPSC)-derived neurons from people with FTLD-tau. Glycogen breakdown redirects glucose flux to the pentose phosphate pathway and alleviates oxidative stress. Our findings uncover a critical role for the neuroprotective effects of dietary restriction (DR) by increasing glycogen breakdown. Mechanistically, we show a potential interaction between tau protein and glycogen, suggesting a vicious cycle in which tau binding promotes glycogen accumulation in neurons, which in turn exacerbates tau accumulation which further disrupts cellular homeostasis. Our studies identify impaired glycogen metabolism as a key hallmark for tauopathies and offer a promising therapeutic target in tauopathy and other neurodegenerative diseases.
tau蛋白病涵盖一系列神经退行性疾病,如阿尔茨海默病(AD)和伴有tau蛋白包涵体的额颞叶变性(FTLD-tau),目前尚无针对这些疾病的有效治疗方法。在此,我们发现tau蛋白病果蝇模型和AD患者大脑中的糖原代谢受损,这表明tau蛋白病与糖原代谢之间存在联系。我们证明,神经元糖原的分解可改善果蝇和FTLD-tau患者诱导多能干细胞(iPSC)衍生神经元中的tau蛋白病表型。糖原分解将葡萄糖通量重定向到磷酸戊糖途径并减轻氧化应激。我们的研究结果揭示了饮食限制(DR)通过增加糖原分解发挥神经保护作用的关键作用。从机制上讲,我们展示了tau蛋白与糖原之间的潜在相互作用,提示了一个恶性循环,即tau蛋白结合促进神经元中糖原积累,进而加剧tau蛋白积累,并进一步破坏细胞内稳态。我们的研究确定糖原代谢受损是tau蛋白病关键标志,并为tau蛋白病和其他神经退行性疾病提供了一个有前景的治疗靶点。