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不对称性脂肪瘤病:两例报告。

Asymmetrical lipomatosis: report of two cases.

作者信息

Enzi G, Digito M, Baldo Enzi G, Perin B, Fiore D

出版信息

Postgrad Med J. 1985 Sep;61(719):797-800. doi: 10.1136/pgmj.61.719.797.

DOI:10.1136/pgmj.61.719.797
PMID:4059137
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2418415/
Abstract

We report on two patients with an asymmetrical expansion of fat tissue. At computed tomography, lipomatous tissue proved to be superficially located in one patient and both subcutaneously and deeply located in the second. Signs and symptoms of a peripheral neuropathy were observed in both patients, who were otherwise asymptomatic. The lipolytic activity in post-heparin plasma was normal in both patients. The fat cell size of lipomatous tissue, obtained in one patient by percutaneous needle biopsy, was higher than that of contralateral, uninvolved adipose tissue. The adipose tissue lipoprotein lipase activity in lipomatous tissue was higher than that in normal tissue. High density lipoprotein (HDL), HDL2 and HDL3 cholesterol values were elevated in both patients but not exceeding 1 standard deviation the values of age and sex matched controls. Isoprenaline-stimulated lipid mobilization was similar in lipomatous and in control tissue.

摘要

我们报告了两名脂肪组织不对称扩张的患者。在计算机断层扫描中,一名患者的脂肪瘤组织位于浅表,另一名患者的脂肪瘤组织则同时位于皮下和深部。两名患者均观察到周围神经病变的体征和症状,除此之外无其他症状。两名患者肝素后血浆中的脂解活性均正常。通过经皮针吸活检从一名患者获取的脂肪瘤组织的脂肪细胞大小高于对侧未受累的脂肪组织。脂肪瘤组织中的脂肪组织脂蛋白脂肪酶活性高于正常组织。两名患者的高密度脂蛋白(HDL)、HDL2和HDL3胆固醇值均升高,但不超过年龄和性别匹配对照组数值的1个标准差。异丙肾上腺素刺激的脂质动员在脂肪瘤组织和对照组织中相似。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/b7becc3b846d/postmedj00115-0031-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/146538132d7c/postmedj00115-0030-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/5411611621e7/postmedj00115-0031-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/711b67e22922/postmedj00115-0031-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/b7becc3b846d/postmedj00115-0031-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/146538132d7c/postmedj00115-0030-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/5411611621e7/postmedj00115-0031-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/711b67e22922/postmedj00115-0031-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1f27/2418415/b7becc3b846d/postmedj00115-0031-c.jpg

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引用本文的文献

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Adult-onset Asymmetrical Lipomatosis.成人起病型不对称性脂肪过多症。
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2
Shoulder girdle lipomatosis.
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Metabolic abnormalities in multiple symmetric lipomatosis: elevated lipoprotein lipase activity in adipose tissue with hyperalphalipoproteinemia.
J Lipid Res. 1983 May;24(5):566-74.
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Mediastino-abdominal lipomatosis: deep accumulation of fat mimicking a respiratory disease and ascites. Clinical aspects and metabolic studies in vitro.
Q J Med. 1984 Autumn;53(212):453-63.
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Multiple symmetric lipomatosis: an updated clinical report.多发性对称性脂肪瘤病:最新临床报告
Medicine (Baltimore). 1984 Jan;63(1):56-64. doi: 10.1097/00005792-198401000-00004.
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Benign symmetric lipomatosis (Launois-Bensaude adenolipomatosis) with gout and hyperlipoproteinemia.伴有痛风和高脂蛋白血症的良性对称性脂肪瘤病(洛努瓦-本索德腺脂肪瘤病)
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