Birt-Hogg-Dubé综合征病例的麻醉管理
Anesthetic management for Birt-Hogg-Dubé syndrome case.
作者信息
Mahmoud Ramy
机构信息
Department of Anaesthesia, Senior Clinical Fellow of Anaesthesia, Kingston Hospital NHS Foundation Trust, London, United Kingdom.
出版信息
Saudi J Anaesth. 2025 Jul-Sep;19(3):419-421. doi: 10.4103/sja.sja_612_24. Epub 2025 Jun 16.
Abstract
Birt-Hogg-Dubé (BHD) syndrome is a rare syndrome which is usually inherited but may occur . It usually presents with cutaneous manifestations, pneumothorax, and, most importantly, renal tumors. Spinal anesthesia was used in this case to avoid respiratory complications such as pneumothorax.
摘要
Birt-Hogg-Dubé（BHD）综合征是一种罕见的综合征，通常为遗传性，但也可能散发。它通常表现为皮肤表现、气胸，最重要的是肾肿瘤。该病例使用了脊髓麻醉以避免诸如气胸等呼吸并发症。
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Birt-Hogg-Dubé syndrome.Birt-Hogg-Dubé 综合征。
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Birt-Hogg-Dubé syndrome, a genodermatosis associated with spontaneous pneumothorax and kidney neoplasia, maps to chromosome 17p11.2.Birt-Hogg-Dubé综合征是一种与自发性气胸和肾肿瘤相关的遗传性皮肤病，定位于染色体17p11.2。
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