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一名患有埃利斯-范克里维尔德综合征和复杂心脏畸形的儿科患者的麻醉管理挑战：病例报告

Anesthetic management challenges in a pediatric patient with Ellis Van Creveld syndrome and complex cardiac anomalies: A case report.

作者信息

Maddali Madan Mohan, Ghafri Mohammed Al

机构信息

Department of Cardiothoracic Anesthesia, National Heart Center, The Royal Hospital, Muscat, Oman.

Department of Pediatric Intensive Care, National Heart Center, The Royal Hospital, Muscat, Oman.

出版信息

Saudi J Anaesth. 2025 Jul-Sep;19(3):395-399. doi: 10.4103/sja.sja_485_24. Epub 2025 Jun 16.

DOI:10.4103/sja.sja_485_24
PMID:40642628
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12240526/
Abstract

The case report discusses the anesthetic management and postoperative course of a 4-month-old girl with Ellis Van Creveld syndrome. Key challenges included an abnormal chest wall, tracheal abnormalities, and complex cardiac issues, requiring tailored anesthetic planning and vigilant monitoring. The patient experienced complications such as complete heart block and persistent hypercapnia after the surgery, which required a permanent pacemaker and prolonged noninvasive ventilation, leading to an extended hospital stay.

摘要

该病例报告讨论了一名患有埃利斯-范克里维尔德综合征的4个月大女孩的麻醉管理和术后病程。主要挑战包括胸壁异常、气管异常和复杂的心脏问题，这需要制定个性化的麻醉计划并进行密切监测。患者术后出现了完全性心脏传导阻滞和持续性高碳酸血症等并发症，需要植入永久性起搏器并延长无创通气时间，导致住院时间延长。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/3cfe4f820a91/SJA-19-395-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/a0005c841d67/SJA-19-395-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/50c5634a6cd5/SJA-19-395-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/26bb1b4dbb4d/SJA-19-395-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/8bdad824c55c/SJA-19-395-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/3b62475a586c/SJA-19-395-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/d6ba40f6213f/SJA-19-395-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/3cfe4f820a91/SJA-19-395-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/a0005c841d67/SJA-19-395-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/50c5634a6cd5/SJA-19-395-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/26bb1b4dbb4d/SJA-19-395-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/8bdad824c55c/SJA-19-395-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/3b62475a586c/SJA-19-395-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/d6ba40f6213f/SJA-19-395-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a39b/12240526/3cfe4f820a91/SJA-19-395-g007.jpg

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