Davidson T I, Kissin M W, Bradish C F, Westbury G
Eur J Surg Oncol. 1985 Dec;11(4):381-4.
Maffucci syndrome comprises multiple enchondromas together with cutaneous haemangiomas. Review of the literature shows a 15-20% incidence of sarcomatous change in one or more of the enchondromas. Malignancy arising from the vascular component, however, has only been reported in one case. We present a further case where a patient with Maffucci syndrome presented with multifocal angiosarcoma.
马富西综合征包括多发性内生软骨瘤和皮肤血管瘤。文献回顾显示，在一个或多个内生软骨瘤中，肉瘤样变的发生率为15% - 20%。然而，仅1例报告了血管成分发生的恶性肿瘤。我们在此报告另一例马富西综合征患者发生多灶性血管肉瘤的病例。
