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一名年轻男性的平山病：病例报告

Hirayama Disease in a Young Male: A Case Report.

作者信息

Paudel Suman, Rokaha Prerana Singh, Rokaha Pratik Singh, Karki Lalit, Thapa Paras

机构信息

Department of Radiology, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.

Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.

出版信息

JNMA J Nepal Med Assoc. 2024 Nov;62(279):770-773. doi: 10.31729/jnma.8804. Epub 2024 Nov 30.

DOI:10.31729/jnma.8804
PMID:40656801
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11931337/
Abstract

Hirayama disease is a rare benign neurological disease that affects the anterior horn of the spinal cord at C5 to T1, mainly at C7 and C8 due to imbalance growth between the vertebral column and the dura mater leading to microcirculatory disturbances in the anterior portion of the spinal cord due to overstretched cord, especially during flexion of the neck causing unilateral or rarely asymmetrically bilateral upper limb weakness and muscle wasting. It is a case of a 21-year-old boy presented with weaknesses in his left hand and forearm for 2 years which aggravates during cold weather and flexion of the neck. A plain x-ray of the neck and MRI of the cervical spine were conducted which show the features of Hirayama disease.

摘要

平山病是一种罕见的良性神经系统疾病，它影响脊髓颈5至胸1节段的前角，主要累及颈7和颈8节段，原因是脊柱与硬脊膜之间生长不平衡，导致脊髓前部因过度伸展而出现微循环障碍，尤其是在颈部屈曲时，会引起单侧或极少出现的不对称双侧上肢无力和肌肉萎缩。这是一名21岁男孩的病例，他左手和前臂无力已有2年，在寒冷天气和颈部屈曲时症状加重。进行了颈部X线平片和颈椎磁共振成像检查，结果显示出平山病的特征。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/d041286cadd8/JNMA-62-279-770-g4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/61baa9f75750/JNMA-62-279-770-g1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/dbf0449f88ed/JNMA-62-279-770-g2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/e35f85ba373d/JNMA-62-279-770-g3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/d041286cadd8/JNMA-62-279-770-g4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/61baa9f75750/JNMA-62-279-770-g1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/dbf0449f88ed/JNMA-62-279-770-g2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/e35f85ba373d/JNMA-62-279-770-g3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8e4/11931337/d041286cadd8/JNMA-62-279-770-g4.jpg

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本文引用的文献

1
Update on the Pathogenesis, Clinical Diagnosis, and Treatment of Hirayama Disease.平山病的发病机制、临床诊断及治疗进展
Front Neurol. 2022 Feb 1;12:811943. doi: 10.3389/fneur.2021.811943. eCollection 2021.
2
Monomelic Amyotrophy (Hirayama Disease): A Rare Case Report and Literature Review.单肢肌萎缩症（平山病）：一例罕见病例报告及文献综述
Case Rep Neurol. 2020 Sep 17;12(3):291-298. doi: 10.1159/000508994. eCollection 2020 Sep-Dec.
3
Monomelic amyotrophy (hirayama disease) with upper motor neuron signs: a case report.伴有上运动神经元体征的单肢肌萎缩症（平山病）：一例报告
Ann Rehabil Med. 2015 Feb;39(1):122-7. doi: 10.5535/arm.2015.39.1.122. Epub 2015 Feb 28.
4
How does the neck flexion affect the cervical MRI features of Hirayama disease?颈屈位如何影响平山病的颈椎 MRI 特征？
Neurol Sci. 2012 Oct;33(5):1101-5. doi: 10.1007/s10072-011-0912-x. Epub 2012 Jan 3.
5
Hirayama disease.平山病。
Neuroimaging Clin N Am. 2011 Nov;21(4):939-50, ix-x. doi: 10.1016/j.nic.2011.07.009.
6
Cervical flexion myelopathy in a patient showing apparent long tract signs: a severe form of Hirayama disease.颈椎过伸性脊髓病伴明显长束征表现的患者：平山病的严重型。
Joint Bone Spine. 2011 May;78(3):316-8. doi: 10.1016/j.jbspin.2010.12.008. Epub 2011 Jan 26.
7
Nationwide survey of juvenile muscular atrophy of distal upper extremity (Hirayama disease) in Japan.日本全国范围内青少年上肢远端型肌肉萎缩症（平山病）调查。
Amyotroph Lateral Scler. 2006 Mar;7(1):38-45. doi: 10.1080/14660820500396877.
8
Focal cervical poliopathy causing juvenile muscular atrophy of distal upper extremity: a pathological study.导致青少年上肢远端肌肉萎缩的局灶性颈段脊髓灰质炎：一项病理学研究
J Neurol Neurosurg Psychiatry. 1987 Mar;50(3):285-90. doi: 10.1136/jnnp.50.3.285.
9
[A cervical collar therapy for non-progressive juvenile spinal muscular atrophy of the distal upper limb (Hirayama's disease)].[一种针对上肢远端非进行性少年型脊髓性肌萎缩症（平山病）的颈托治疗方法]
Rinsho Shinkeigaku. 1992 Oct;32(10):1102-6.