Paudel Suman, Rokaha Prerana Singh, Rokaha Pratik Singh, Karki Lalit, Thapa Paras
Department of Radiology, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
JNMA J Nepal Med Assoc. 2024 Nov;62(279):770-773. doi: 10.31729/jnma.8804. Epub 2024 Nov 30.
Hirayama disease is a rare benign neurological disease that affects the anterior horn of the spinal cord at C5 to T1, mainly at C7 and C8 due to imbalance growth between the vertebral column and the dura mater leading to microcirculatory disturbances in the anterior portion of the spinal cord due to overstretched cord, especially during flexion of the neck causing unilateral or rarely asymmetrically bilateral upper limb weakness and muscle wasting. It is a case of a 21-year-old boy presented with weaknesses in his left hand and forearm for 2 years which aggravates during cold weather and flexion of the neck. A plain x-ray of the neck and MRI of the cervical spine were conducted which show the features of Hirayama disease.
平山病是一种罕见的良性神经系统疾病,它影响脊髓颈5至胸1节段的前角,主要累及颈7和颈8节段,原因是脊柱与硬脊膜之间生长不平衡,导致脊髓前部因过度伸展而出现微循环障碍,尤其是在颈部屈曲时,会引起单侧或极少出现的不对称双侧上肢无力和肌肉萎缩。这是一名21岁男孩的病例,他左手和前臂无力已有2年,在寒冷天气和颈部屈曲时症状加重。进行了颈部X线平片和颈椎磁共振成像检查,结果显示出平山病的特征。