Sharma Arun, Garg Dollphy, Aggarwal Pankaj, Singhal Manphool
Department of Radiodiagnosis, PGIMER, Chandigarh, -160012 India.
Department of Cardiothoracic and Vascular Surgery, PGIMER, Chandigarh, -160012 India.
Indian J Thorac Cardiovasc Surg. 2025 Aug;41(8):1051-1054. doi: 10.1007/s12055-025-01912-z. Epub 2025 Feb 27.
Total anomalous pulmonary venous drainage (TAPVC) is a rare congenital anomaly with drainage of all the pulmonary veins into the systemic circulation instead of the left atrium. The commonest anomalous pattern of supracardiac TAPVC includes formation of the left-sided vertical vein draining into the left brachiocephalic vein. All the pulmonary veins forming a right-sided vertical vein and draining into proximal superior vena cava (SVC) are a highly uncommon variant, with distinct anatomical course. We present an extremely rare case of an 8-month-old child who presented with a variant pattern of drainage, and was managed successfully.
完全性肺静脉异位引流(TAPVC)是一种罕见的先天性畸形,所有肺静脉引流至体循环而非左心房。心上型TAPVC最常见的异常模式包括形成引流至左头臂静脉的左侧垂直静脉。所有肺静脉形成右侧垂直静脉并引流至近端上腔静脉(SVC)是一种非常罕见的变异,具有独特的解剖路径。我们报告一例极其罕见的8个月大儿童病例,其呈现出一种变异的引流模式,并成功得到治疗。