Duriqi Adnan, Dedushi Hoti Kreshnike, Gocaj Kaltrina, Hyseni Fjolla
University Clinical Center of Kosova, Euromed Hospital, Fushe Kosove, Prishtine, Kosovo, Albania.
Department of Radiology, Faculty of Medicine, University of Prishtina "Hasan Prishtina", Prishtine, Kosovo, Albania.
J Clin Imaging Sci. 2025 Jun 18;15:22. doi: 10.25259/JCIS_138_2024. eCollection 2025.
Syringomyelia is a rare condition characterized by the formation of a fluid-filled cyst within the spinal cord, leading to myelopathy. In addition, the pathological enlargement of the central canal is referred to as hydromyelia or cleft-like syrinx. We present a case of idiopathic syringomyelia and hematomyelia in a 50-year-old female patient with a 5-year follow-up on her disease progression. Magnetic resonance imaging (MRI) images revealed low-signal intensity on T1 and high-signal intensity on T2, with elevated hemorrhagic signal intensity on T1 and low peripheral signal intensity on T2. A fluid-filled lesion measuring 12 × 36 mm was observed between the C7 and Th3 vertebrae, with separation from some of the detailed components. No contrast enhancement was noted following IV contrast administration. Based on the MRI findings, a diagnosis consistent with giant hemorrhagic syringomyelia was established. Subsequently, a neurosurgical intervention was performed, resulting in a reduction in the size of the syringomyelia and a moderate improvement in the patient's symptom profile.
脊髓空洞症是一种罕见病症，其特征为脊髓内形成充满液体的囊肿，进而导致脊髓病。此外，中央管的病理性扩大被称为积水性脊髓空洞症或裂隙样空洞。我们报告一例50岁女性特发性脊髓空洞症和脊髓出血性病变的病例，并对其疾病进展进行了5年随访。磁共振成像（MRI）图像显示，T1加权像呈低信号强度，T2加权像呈高信号强度，T1加权像上出血信号强度升高，T2加权像上周边信号强度降低。在C7和Th3椎体之间观察到一个大小为12×36毫米的充满液体的病变，与一些详细结构分离。静脉注射造影剂后未观察到对比增强。根据MRI结果，确诊为巨大出血性脊髓空洞症。随后进行了神经外科干预，脊髓空洞症体积减小，患者症状有中度改善。
