Lotfian Golnaz, Al-Warqi Akram, Gaddikeri Santhosh, Jhaveri Miral D, Vattoth Surjith
Department of Diagnostic Radiology and Nuclear Medicine, Rush University Medical Center, Chicago, IL, USA.
Neuroradiology. 2025 Aug 7. doi: 10.1007/s00234-025-03727-6.
Craniopharyngiomas are rare, benign tumors with a bimodal age distribution, typically found in children and older adults. They arise along the craniopharyngeal tract, often in the intra- or suprasellar regions, and may compress adjacent structures, causing diverse symptoms. Diagnosis is primarily MRI-based, revealing heterogeneous mass with cystic and solid elements. Chordoma, another rare tumor, arises from notochordal remnants, often in the sacrum or clivus, and displays distinct imaging characteristics like T2 hyperintensity and bony destruction. This report discusses a rare ectopic clival craniopharyngioma in an 11-year-old- the youngest case reported in the literature to our knowledge -extending from the sellar to the clival region. Noteworthy imaging findings included T1 hyperintensity and a downward growth pattern along the expected Rathke pouch course, helping distinguish it from chordoma.
颅咽管瘤是一种罕见的良性肿瘤，具有双峰年龄分布，通常见于儿童和老年人。它们沿颅咽管发生，常位于鞍内或鞍上区域，并可能压迫相邻结构，导致各种症状。诊断主要基于磁共振成像（MRI），显示出具有囊性和实性成分的异质性肿块。脊索瘤是另一种罕见肿瘤，起源于脊索残余组织，常位于骶骨或斜坡，并表现出不同的影像学特征，如T2高信号和骨质破坏。本报告讨论了一例11岁儿童罕见的异位斜坡颅咽管瘤——据我们所知，这是文献报道中最年轻的病例——肿瘤从鞍区延伸至斜坡区。值得注意的影像学表现包括T1高信号以及沿预期的拉特克囊路径向下生长的模式，这有助于将其与脊索瘤区分开来。
