Lang D, Wagenvoort C A, Kupferschmid C, Kleihauer E
Pediatr Cardiol. 1985;6(3):161-4. doi: 10.1007/BF02336557.
In a 17-month-old boy with clinical signs of right heart failure, the diagnosis of primary pulmonary hypertension was made, based on cardiac catheterization findings with high pulmonary arterial pressure and normal pulmonary wedge pressure although two-dimensional echocardiography demonstrated a left atrial membrane. Postmortem examination confirmed a left atrial membrane (cor triatriatum), and the microscopic examination revealed the histological pattern of primary pulmonary hypertension. Due to reduced pulmonary blood flow, pulmonary venous obstruction was masked and could not be assessed by measuring pulmonary wedge pressure.
一名17个月大的男童出现右心衰竭的临床症状，基于心导管检查结果（肺动脉压高而肺楔压正常）诊断为原发性肺动脉高压，尽管二维超声心动图显示有左房隔膜。尸检证实存在左房隔膜（三房心），显微镜检查显示出原发性肺动脉高压的组织学模式。由于肺血流量减少，肺静脉阻塞被掩盖，无法通过测量肺楔压进行评估。
