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以神经精神症状为表现的类脂蛋白沉积症。

Lipoid proteinosis presenting with neuropsychiatric manifestations.

作者信息

Emsley R A, Paster L

出版信息

J Neurol Neurosurg Psychiatry. 1985 Dec;48(12):1290-2. doi: 10.1136/jnnp.48.12.1290.

DOI:10.1136/jnnp.48.12.1290
PMID:4087005
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1028616/
Abstract

Two patients with lipoid proteinosis are reported in whom paranoid symptoms were the presenting feature. Both had a long standing impairment of memory and bilateral medial temporal lobe calcification demonstrated by CT scan. Possible associations between the anatomical site of these lesions and the neuropsychiatric manifestations are discussed.

摘要

报告了两名患有类脂蛋白沉积症的患者，其首发症状为偏执症状。两人均有长期的记忆损害，CT扫描显示双侧颞叶内侧钙化。讨论了这些病变的解剖部位与神经精神表现之间可能的关联。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bc7/1028616/3dea2f5320a2/jnnpsyc00116-0099-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bc7/1028616/3dea2f5320a2/jnnpsyc00116-0099-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bc7/1028616/3dea2f5320a2/jnnpsyc00116-0099-a.jpg

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