Mazurczyk Łukasz, Czarnogórski Michał, Czernicka Aleksandra, Lipowski Paweł, Ostrowski Adam, Juszczak Kajetan, Adamowicz Jan, Drewa Tomasz
Department and Chair of Urology and Andrology, Ludwik Rydygier Collegium Medicum, Nicolaus Copernicus University, Bydgoszcz, Poland.
Cent European J Urol. 2025;78(2):103-108. doi: 10.5173/ceju.2024.0280. Epub 2025 Apr 28.
Urinary bladder leiomyosarcoma is an extremely rare malignancy of the urogenital system. We present the case of a 59-year-old Caucasian male with a gigantic bladder leiomyosarcoma. The patient was subdued to the surgical excision of the urinary bladder - laparoscopic radical cystectomy with extended pelvic lymphadenectomy, with urinary diversion by bilateral ureterocutaneostomy. The excision was complete both macroscopically and microscopically. No additional adjuvant therapy was administered. In the 6-month follow-up, the patient remained in radiological remission. Surgical excision with extended pelvic lymphadenectomy seems to be sufficient in the treatment of urinary bladder leiomyosarcoma.
膀胱平滑肌肉瘤是泌尿生殖系统极为罕见的恶性肿瘤。我们报告一例59岁白种男性患有巨大膀胱平滑肌肉瘤的病例。该患者接受了膀胱手术切除——腹腔镜根治性膀胱切除术并扩大盆腔淋巴结清扫术,通过双侧输尿管皮肤造口术进行尿流改道。切除在宏观和微观层面均完整。未给予额外的辅助治疗。在6个月的随访中,患者处于影像学缓解状态。扩大盆腔淋巴结清扫术的手术切除似乎足以治疗膀胱平滑肌肉瘤。