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Radiological changes in STING-associated vasculopathy of infancy treated with a JAK inhibitor.

作者信息

Sato Tomomi, Nagatani Yukihiro, Hirota Yukiko, Kunitsu Tomoaki, Maruo Yoshihiro

机构信息

Clinical Education Center for Physicians, Shiga University of Medical Science, Otsu, Shiga, Japan.

Department of Pediatrics, Shiga University of Medical Science, Otsu, Shiga, Japan.

出版信息

Pediatr Int. 2025 Jan-Dec;67(1):e70148. doi: 10.1111/ped.70148.

DOI:10.1111/ped.70148
PMID:40874483
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12392380/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8446/12392380/4034ad5a774b/PED-67-e70148-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8446/12392380/4034ad5a774b/PED-67-e70148-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8446/12392380/4034ad5a774b/PED-67-e70148-g001.jpg

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本文引用的文献

1
Janus Kinase Inhibitors in the Treatment of Type I Interferonopathies: A Case Series From a Single Center in China.Janus 激酶抑制剂治疗 I 型干扰素病：来自中国单一中心的病例系列。
Front Immunol. 2022 Mar 28;13:825367. doi: 10.3389/fimmu.2022.825367. eCollection 2022.
2
The 2021 European Alliance of Associations for Rheumatology/American College of Rheumatology Points to Consider for Diagnosis and Management of Autoinflammatory Type I Interferonopathies: CANDLE/PRAAS, SAVI, and AGS.2021年欧洲风湿病协会联盟/美国风湿病学会关于I型干扰素病（包括CANDLE/PRAAS、SAVI和AGS）诊断和管理的考虑要点
Arthritis Rheumatol. 2022 May;74(5):735-751. doi: 10.1002/art.42087. Epub 2022 Mar 21.
3
Severe Liver Disorder Following Liver Transplantation in STING-Associated Vasculopathy with Onset in Infancy.
婴儿期起病的 STING 相关性血管病肝移植后严重肝脏疾病
J Clin Immunol. 2021 Jul;41(5):967-974. doi: 10.1007/s10875-021-00977-w. Epub 2021 Feb 5.
4
Overview of STING-Associated Vasculopathy with Onset in Infancy (SAVI) Among 21 Patients.21 例婴儿起病的 STING 相关性血管病（SAVI）概述。
J Allergy Clin Immunol Pract. 2021 Feb;9(2):803-818.e11. doi: 10.1016/j.jaip.2020.11.007. Epub 2020 Nov 18.
5
Efficacy and Adverse Events During Janus Kinase Inhibitor Treatment of SAVI Syndrome.Janus 激酶抑制剂治疗 SAVI 综合征的疗效和不良事件。
J Clin Immunol. 2019 Jul;39(5):476-485. doi: 10.1007/s10875-019-00645-0. Epub 2019 May 29.
6
Efficacy of the Janus kinase 1/2 inhibitor ruxolitinib in the treatment of vasculopathy associated with TMEM173-activating mutations in 3 children.Janus激酶1/2抑制剂芦可替尼治疗3例与TMEM173激活突变相关的血管病变患儿的疗效
J Allergy Clin Immunol. 2016 Dec;138(6):1752-1755. doi: 10.1016/j.jaci.2016.07.015. Epub 2016 Aug 20.
7
Activated STING in a vascular and pulmonary syndrome.激活 STING 与血管和肺部综合征相关。
N Engl J Med. 2014 Aug 7;371(6):507-518. doi: 10.1056/NEJMoa1312625. Epub 2014 Jul 16.