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巨大带蒂胸壁肿瘤40余年演变的罕见病因:1例报告

Exceptional etiology of a huge pedunculated chest wall tumor with over 40 years of evolution: A case report.

作者信息

Chaari Zied, Ayed Aymen Ben, Bouattour Hanen, Ayed Ahmed Ben, Hentati Abdessalem

机构信息

University of Sfax-Habib Bourguiba University Hospital, Department of Thoracic and Cardiovascular Surgery, Sfax, Tunisia.

University of Sfax-Habib Bourguiba University Hospital, Department of Thoracic and Cardiovascular Surgery, Sfax, Tunisia.

出版信息

Int J Surg Case Rep. 2025 Oct;135:111898. doi: 10.1016/j.ijscr.2025.111898. Epub 2025 Sep 4.

DOI:10.1016/j.ijscr.2025.111898
PMID:40914094
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12450564/
Abstract

INTRODUCTION AND IMPORTANCE

Chest wall tumors are common and predominantly benign. Exceptionally, long-standing evolution over decades can lead to the development of giant tumors, posing substantial technical and strategic challenges in determining the optimal surgical approach.

PRESENTATION OF CASE

We report a rare case of a giant pedunculated chest wall lipoma that had been growing for over 40 years in a 73-year-old man. CT scan revealed a mass with a 5 cm-suprascapular-implantation base, hanging posteriorly and mimicking a pseudo-limb, measuring 17 × 7 cm in diameter and 34 cm in length. Complete surgical resection was performed, and histopathology confirmed a benign lipoma with no signs of malignancy.

CLINICAL DISCUSSION

To our knowledge, this is the first reported case of a huge lipoma with more than 40 years of evolution and an unusual pedunculated presentation resembling a third upper limb.

CONCLUSION

This case is exceptional due to its pedunculated appearance resembling an additional limb, and a slow evolution over more than 40 years. Complete surgical resection ensures a favorable prognosis.

摘要

引言与重要性

胸壁肿瘤较为常见,且大多为良性。极少数情况下,数十年的长期发展可导致巨大肿瘤的形成,这在确定最佳手术方法时带来了重大的技术和策略挑战。

病例介绍

我们报告一例罕见的巨大带蒂胸壁脂肪瘤病例,该脂肪瘤在一名73岁男性体内生长超过40年。CT扫描显示一个肿块,肩胛上植入基底为5厘米,向后悬挂,形似假肢体,直径为17×7厘米,长度为34厘米。进行了完整的手术切除,组织病理学证实为良性脂肪瘤,无恶性迹象。

临床讨论

据我们所知,这是首例报道的具有40多年演变且呈现出类似第三条上肢的不寻常带蒂表现的巨大脂肪瘤病例。

结论

该病例因其带蒂外观类似额外肢体以及超过40年的缓慢演变而格外特殊。完整的手术切除可确保良好的预后。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/d6c54d9db60a/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/ca022cd22217/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/fb5ee9e2c89d/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/d6c54d9db60a/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/ca022cd22217/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/fb5ee9e2c89d/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2589/12450564/d6c54d9db60a/gr3.jpg

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