Jacoby C G, Go R T, Hahn F J
AJR Am J Roentgenol. 1977 Jul;129(1):5-9. doi: 10.2214/ajr.129.1.5.
The clinical and radiographic findings in four cases of cerebral hemiatrophy are presented. CT findings reflect the underlying gross pathologic changes and are in agreement with those seen on plain skull radiography and pneumoencephalography. The most impressive finding was unilateral loss of cerebral volume with ipsilateral displacement of the midline structures. The differential diagnosis primarily includes Sturge-Weber syndrome and linear sebaceous nevus syndrome. The recognition of compensatory calvarial changes should indicate that the cerebral abnormalities are the result of an atrophic or hypoplastic process that began in early life.
本文报告了4例大脑半球萎缩的临床和影像学表现。CT表现反映了潜在的大体病理变化,与头颅平片和气脑造影所见相符。最显著的发现是单侧脑容量减少,中线结构向同侧移位。鉴别诊断主要包括斯特奇-韦伯综合征和线性皮脂腺痣综合征。认识到颅骨的代偿性变化应提示大脑异常是始于早年的萎缩或发育不全过程的结果。