Rosenfield A T, Siegel N J, Kappelman N B, Taylor K J
AJR Am J Roentgenol. 1977 Aug;129(2):297-303. doi: 10.2214/ajr.129.2.297.
The gray scale ultrasound findings of three patients with medullary cystic disease of the kidney and two patients with congenital hepatic fibrosis with tubular ectasia are reported. Medullary cystic disease of the kidney typically presents early in adulthood with renal failure and salt-losing nephropathy. The spectrum of gray scale ultrasound findings in this entity includes irregular widened central echoes when small cysts are present and well defined cystic structures when larger medullary cysts are the predominant lesion. The ultrasound findings in congenital hepatic fibrosis with tubular ectasia seem to be a characteristic combination of nephromegaly, a distorted renal echo pattern, and high level echoes in the liver. Ultrasound is a useful noninvasive method which is complementary to other methods in the identification and differential diagnosis of bilateral renal cystic disease.
报告了3例肾髓质囊性疾病患者和2例伴有肾小管扩张的先天性肝纤维化患者的灰阶超声检查结果。肾髓质囊性疾病通常在成年早期出现肾衰竭和失盐性肾病。该疾病的灰阶超声表现范围包括存在小囊肿时中央回声不规则增宽，以及以较大的髓质囊肿为主时边界清晰的囊性结构。伴有肾小管扩张的先天性肝纤维化的超声表现似乎是肾肿大、肾回声模式扭曲以及肝脏内高回声的特征性组合。超声是一种有用的非侵入性方法，在双侧肾囊性疾病的识别和鉴别诊断中可作为其他方法的补充。
