Taha Attaa K, Abdelaziz Ismaiel Mahmoud, Amer Rana M, Hesham Hammad Ahmed, Naji Hayder
Imaging, University of Baghdad College of Medicine, Baghdad, IRQ.
Cardiovascular Medicine, Global Medical City Hospital, Cairo, EGY.
Cureus. 2025 Aug 6;17(8):e89496. doi: 10.7759/cureus.89496. eCollection 2025 Aug.
Cor triatriatum is a rare congenital heart defect that divides the right or left atrium into three chambers. Although the diagnosis is typically made within the first years of birth, it can occasionally be made later in adulthood and is frequently associated with other cardiac defects but may be present in isolation. Clinical manifestations range from lung congestion, exhaustion, coughing, and dyspnea to the onset of heart failure. The treatment depends on the existence of symptoms; asymptomatic patients need only regular follow-up, while symptomatic patients require intervention either surgically or percutaneously. We present a case of an adult patient who presented to us with a manifestation of decompensated right-sided heart failure, and upon investigation, we incidentally discovered that she had a rare congenital heart defect, a non-fenestrated isolated cor triatriatum dexter (CTD) not associated with the tricuspid valve defect or other congenital heart defects. Right-sided heart failure has developed as a complication of CTD. Additionally, this case highlights the diagnostic value of transthoracic echocardiography in adult congenital heart disease.
三房心是一种罕见的先天性心脏缺陷，它将右心房或左心房分为三个腔室。虽然诊断通常在出生后的头几年内做出，但偶尔也可能在成年后期做出，并且常与其他心脏缺陷相关，但也可能单独存在。临床表现从肺充血、乏力、咳嗽和呼吸困难到心力衰竭的发作不等。治疗取决于症状的存在；无症状患者仅需定期随访，而有症状患者则需要手术或经皮干预。我们报告一例成年患者，该患者因失代偿性右心衰竭表现前来就诊，经检查，我们偶然发现她患有一种罕见的先天性心脏缺陷，即非开窗型孤立性右三房心（CTD），与三尖瓣缺陷或其他先天性心脏缺陷无关。右心衰竭已发展为CTD的并发症。此外，该病例突出了经胸超声心动图在成人先天性心脏病中的诊断价值。
