Qin Huanyu, Jiang Nan, Qin Siyang, Tang Yipeng, Chen Tongyun
Department of Cardiac Surgery, Chest Hospital, Tianjin University, Tianjin, China.
Medicine (Baltimore). 2025 Sep 5;104(36):e44213. doi: 10.1097/MD.0000000000044213.
Tracheomalacia, typically seen in relapsing polychondritis,[1] is rarely reported in association with congenital heart disease (CHD). In patients with pulmonary hypoperfusion-type CHD, surgical repair results in a rapid increase in pulmonary blood flow, predisposing them to mucus retention, airway obstruction, and respiratory distress. We describe acute airway collapse in a patient with double outlet right ventricle and congenital bronchial stenosis following cardiac repair. Surgically augmented pulmonary flow critically narrowed the stenotic airway, rapidly reversed by bronchoscopic stenting. We introduce the concept of "hemodynamic-aggravated airway compromise" and advocate for protocolized monitoring in CHD-airway comorbidity cases.
A 19-year-old male with double outlet right ventricle and pulmonary stenosis underwent a central aortopulmonary shunt. Asymptomatic left main bronchial stenosis was incidentally found on preoperative CT. Four hours post-extubation, he developed acute respiratory distress. A bronchial stent was placed on postoperative day 10, resulting in marked clinical improvement and eventual discharge.
Stenosis of the left main bronchus and left upper lobe bronchus was noted on preoperative chest CT. Postoperative increases in pulmonary blood flow and mucus retention were thought to contribute to secondary airway obstruction. Bronchoscopy demonstrated significant luminal obstruction of the bronchus.
An airway stent was successfully deployed in the left main bronchus under bronchoscopic guidance. The patient recovered with comprehensive management including airway care, antimicrobial therapy, and inotropic support.
Spontaneous breathing resumed on postoperative day 4 following stent placement; decannulation occurred day 10, and multidisciplinary discharge occurred on day 18 with stable cardiopulmonary status.
In patients who experience postoperative failure to liberate from mechanical ventilation accompanied by recurrent mucus retention, the possibility of underlying structural airway abnormalities should be carefully considered. Early evaluation with bronchoscopy and cross-sectional airway imaging is warranted for timely and accurate diagnosis. Once the anatomic obstruction is confirmed, bronchial stent placement represents a feasible, effective, and controllable therapeutic strategy. Rigorous pre-procedural assessment of indications and vigilant postoperative surveillance are essential to minimize the risk of stent-related complications.
气管软化通常见于复发性多软骨炎[1],与先天性心脏病(CHD)相关的报道很少。在肺血流灌注不足型CHD患者中,手术修复会导致肺血流量迅速增加,使他们易发生黏液潴留、气道阻塞和呼吸窘迫。我们描述了1例右心室双出口合并先天性支气管狭窄患者在心脏修复术后发生的急性气道塌陷。手术增加的肺血流量使狭窄气道严重狭窄,通过支气管镜支架置入迅速逆转。我们引入了“血流动力学加重的气道损害”这一概念,并主张对CHD合并气道疾病的病例进行规范化监测。
1例19岁男性,患有右心室双出口和肺动脉狭窄,接受了中心性主肺动脉分流术。术前CT偶然发现无症状的左主支气管狭窄。拔管后4小时,他出现急性呼吸窘迫。术后第10天放置了支气管支架,临床症状明显改善,最终出院。
术前胸部CT显示左主支气管和左上叶支气管狭窄。术后肺血流量增加和黏液潴留被认为是导致继发性气道阻塞的原因。支气管镜检查显示支气管管腔明显阻塞。
在支气管镜引导下成功地在左主支气管置入了气道支架。患者通过包括气道护理、抗菌治疗和强心支持在内的综合管理得以康复。
支架置入术后第4天恢复自主呼吸;第10天拔管,第18天多学科评估后出院,心肺状态稳定。
对于术后未能脱离机械通气并伴有反复黏液潴留的患者,应仔细考虑潜在的结构性气道异常的可能性。有必要早期进行支气管镜检查和气道横断面成像评估,以实现及时准确的诊断。一旦确认存在解剖性梗阻,支气管支架置入是一种可行、有效且可控的治疗策略。严格的术前适应证评估和术后密切监测对于将支架相关并发症的风险降至最低至关重要。