Dobrevski Boban, Willems Hannah, Lossius-Cott Carolin, Müller Jörg P
Institute of Molecular Cell Biology, Center for Molecular Biomedicine, University Hospital of Friedrich Schiller University, 07745 Jena, Germany.
Institute of Immunobiology and Human Genetics, Faculty of Medicine, Ss. Cyril and Methodius University in Skopje, 1000 Skopje, North Macedonia.
Cancers (Basel). 2025 Sep 7;17(17):2931. doi: 10.3390/cancers17172931.
Fms-like tyrosine kinase 3 (FLT3) is a receptor tyrosine kinase (RTK) that is involved in cell survival, proliferation, and differentiation of haematopoietic progenitors of lymphoid and myeloid lineages. Oncogenic mutations in the FLT3 gene, resulting in constitutively active FLT3 variants, are frequently found in patients with acute myeloid leukaemia (AML). In particular, patients expressing FLT3 ITD (internal tandem duplications of the juxtamembrane domain of FLT3) correlate with poor patient survival. Targeting FLT3-mutated leukaemic stem cells is therefore a key to the efficient treatment of patients with relapsed/refractory AML. The efficacy of approved tyrosine kinase inhibitors is regularly compromised by various resistance pathways or secondary mutations. Based on the current molecular understanding of aberrant signal transduction pathways and cell transformation, novel alternative treatment approaches can be exploited for therapeutic purposes. In particular, new insights into the regulation of the activity of counteracting protein tyrosine phosphatases (PTPs), the aberrant biogenesis and activation of mutant FLT3 proteins, as well as common factors controlling cell transformation are attractive avenues. This review summarises the current knowledge about the regulation of the oncogenic activities of mutant FLT3 proteins and discusses possible options for alternative treatments.
Fms样酪氨酸激酶3(FLT3)是一种受体酪氨酸激酶(RTK),参与淋巴细胞系和髓细胞系造血祖细胞的存活、增殖和分化。FLT3基因的致癌突变会导致组成型活性FLT3变体,在急性髓系白血病(AML)患者中经常发现。特别是,表达FLT3内部串联重复(ITD,FLT3近膜结构域的内部串联重复)的患者生存率较差。因此,靶向FLT3突变的白血病干细胞是有效治疗复发/难治性AML患者的关键。已批准的酪氨酸激酶抑制剂的疗效经常受到各种耐药途径或二次突变的影响。基于目前对异常信号转导途径和细胞转化的分子理解,可以开发新的替代治疗方法用于治疗目的。特别是,对拮抗蛋白酪氨酸磷酸酶(PTP)活性调节、突变FLT3蛋白的异常生物合成和激活以及控制细胞转化的共同因素的新见解是有吸引力的途径。本综述总结了目前关于突变FLT3蛋白致癌活性调节的知识,并讨论了替代治疗的可能选择。