Roopesh Bojja Venkata Satya, Kumar Gowdhaman Anand, Pavithran Sreeja, Agarwal Ravi, Sivakumar Kothandam
Department of Pediatric Cardiology, Institute of Cardiovascular Diseases, The Madras Medical Mission Hospital, Chennai, Tamil Nadu, India.
Ann Pediatr Cardiol. 2025 Mar-Apr;18(2):169-172. doi: 10.4103/apc.apc_42_25. Epub 2025 Aug 29.
Truncus arteriosus (TA) is a major cyanotic heart malformation infrequently associated with aortic arch interruption and isolation of the branch pulmonary artery. Anomalous superior vena caval drainage to the left atrium (LA) is hitherto unreported in TA. In a 45-day-old infant diagnosed with TA and cyanosis, anomalous drainage of the right superior vena cava into the LA was not identified preoperatively or intraoperatively. It was detected postoperatively due to persistent hypoxemia. The anomaly posed unique challenges in the subsequent management. This case report highlights the unusual association of systemic venous drainage in TA.
动脉干（TA）是一种主要的青紫型心脏畸形，很少与主动脉弓中断和分支肺动脉离断相关。上腔静脉异常引流至左心房（LA）在TA中迄今未见报道。在一名诊断为TA并伴有青紫的45日龄婴儿中，术前及术中均未发现右上腔静脉异常引流至LA。术后因持续性低氧血症才检测到该异常。这种异常在后续治疗中带来了独特的挑战。本病例报告强调了TA中体静脉引流的不寻常关联。
