Ayub Muhammad, Ahmed Sobia, La Quang Dai, Krishna Eashwar, Baloch Aiman, Shabbir Shazia, Bashir Sumayya, Rahim Farzana, Pryor Francis
Radiology, Bolan Medical Complex Hospital, Quetta, PAK.
Biology, Texas A&M University, College Station, USA.
Cureus. 2025 Aug 17;17(8):e90330. doi: 10.7759/cureus.90330. eCollection 2025 Aug.
Renal angiomyolipomas (AMLs) are typically benign tumors of the renal cortex, often discovered incidentally. Although rare, AMLs can originate in the renal sinus and extend into the pelvicalyceal system, leading to obstructive uropathy and mimicking urothelial malignancies. We present the case of a 23-year-old female who was referred to our institution with right flank pain and hematuria. Imaging revealed a fat-containing mass in the right renal sinus extending into the pelvicalyceal system and causing ureteropelvic junction obstruction. A presumptive diagnosis of AML was made based on CT characteristics, which was later confirmed histopathologically following surgical excision. This case emphasizes the importance of recognizing the characteristic imaging features of AMLs, particularly in unusual locations, and highlights the role of biopsy in guiding conservative, nephron-sparing management.
肾血管平滑肌脂肪瘤（AMLs）通常是肾皮质的良性肿瘤，常为偶然发现。虽然罕见，但AMLs可起源于肾窦并延伸至肾盂肾盏系统，导致梗阻性尿路病并酷似尿路上皮恶性肿瘤。我们报告一例23岁女性，因右侧腰痛和血尿转诊至我院。影像学检查显示右肾窦内有一含脂肪肿块，延伸至肾盂肾盏系统并导致输尿管肾盂连接处梗阻。根据CT特征作出AML的初步诊断，随后手术切除后经组织病理学证实。该病例强调了认识AML特征性影像学表现的重要性，尤其是在不寻常部位，并突出了活检在指导保守的、保留肾单位治疗中的作用。
