四种溶酶体贮积病中复杂碳水化合物的储存模式：岩藻糖苷贮积症、GM1神经节苷脂贮积症、GM2神经节苷脂贮积症（桑德霍夫变异型）和甘露糖苷贮积症。 - Suppr | 超能文献

Patterns of complex carbohydrate storage in four lysosomal storage diseases: fucosidosis, GM1-gangliosidosis, GM2-gangliosidosis (Sandhoff variant) and mannosidosis.

作者信息

Dawson G, Chen Tsay G

出版信息

Biochem Exp Biol. 1977;13(1):15-25.

Abstract

摘要

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Patterns of complex carbohydrate storage in four lysosomal storage diseases: fucosidosis, GM1-gangliosidosis, GM2-gangliosidosis (Sandhoff variant) and mannosidosis.四种溶酶体贮积病中复杂碳水化合物的储存模式：岩藻糖苷贮积症、GM1神经节苷脂贮积症、GM2神经节苷脂贮积症（桑德霍夫变异型）和甘露糖苷贮积症。

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