Anselmi G, Suárez J A, Machado I, Moleiro F, Blanco P
Br Heart J. 1970 Jul;32(4):575-8. doi: 10.1136/hrt.32.4.575.
A report is made of a rare case of Wilms' tumour which simulated clinically a syndrome of ;right heart failure', as found in some cases of Ebstein's disease. The clinical, radiological, and electrocardiographic study led to the suspicion of this type of malformation. The cine-angiographic study revealed two important facts: the impossibility of approaching the inferior vena cava with opaque material injected into the azygos vein and a filling defect of the right atrium. The post-mortem study revealed the presence of a Wilms' tumour of the right kidney which extended into the inferior vena cava and into the right atrium without producing metastases. This seems to be the first case of this peculiar course of a Wilm's tumour which has grown into the right atrium, resulting in this bizarre clinical picture.
本文报告一例罕见的威尔姆斯瘤病例,该病例临床上模拟了某些埃布斯坦病病例中出现的“右心衰竭”综合征。临床、放射学和心电图研究引发了对这种畸形类型的怀疑。心血管造影研究揭示了两个重要事实:经奇静脉注入不透光物质无法接近下腔静脉,以及右心房存在充盈缺损。尸检研究发现右肾有一个威尔姆斯瘤,它延伸至下腔静脉和右心房,但未发生转移。这似乎是威尔姆斯瘤以这种特殊方式生长至右心房并导致这种奇特临床症状的首例病例。