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Alterations of astrocytic organelles in various lipidoses and allied diseases.

作者信息

Adachi M, Torii J, Karvounis P C, Volk B W

出版信息

Acta Neuropathol. 1971;18(1):74-83. doi: 10.1007/BF00684476.

DOI:10.1007/BF00684476
PMID:4325446
Abstract
摘要

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Acta Neuropathol. 1971;18(1):74-83. doi: 10.1007/BF00684476.
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[Ultrastructural aspects and biochemical significance of metachromatic granulations and other inclusions in cultured fibroblasts from lipidosis and mucopolysaccharidosis].[脂质沉积症和粘多糖贮积症培养成纤维细胞中异染粒及其他包涵体的超微结构特征和生化意义]
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Enzyme replacement treatment for Tay-Sachs disease brain cells in culture utilizing concanavalin A-mediated hexosaminidase A uptake: biochemical and morphological evidence of GM2 mobilization.利用伴刀豆球蛋白A介导的己糖胺酶A摄取对培养的泰-萨克斯病脑细胞进行酶替代治疗:GM2 转运的生化和形态学证据
Acta Neuropathol. 1980;50(1):9-17. doi: 10.1007/BF00688529.
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The AB-variant of GM2-gangliosidosis. Clinical, biochemical, and pathological studies of two patients.GM2神经节苷脂贮积症AB变异型。两名患者的临床、生化及病理研究。
Acta Neuropathol. 1980;52(3):189-202. doi: 10.1007/BF00705807.
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Early central nervous system lesions in experimental hypercholesterolemia in normal and subdiabetic rabbits.

本文引用的文献

1
The enzymic and morphologic organization of the mitochondria.线粒体的酶学和形态学结构
Pediatrics. 1960 Sep;26:466-75.
2
Electron microscopy and the functional significance of a new cellular structure in plasmocytes: a review.浆细胞中一种新细胞结构的电子显微镜观察及其功能意义:综述
Blood. 1955 Jun;10(6):650-4.
3
ULTRASTRUCTURAL AND BIOCHEMICAL OBSERVATIONS ON A CASE OF SYSTEMIC LATE INFANTILE LIPIDOSIS AND ITS RELATIONSHIP TO TAY-SACHS DISEASE AND GARGOYLISM.一例全身性晚发性婴儿脂质沉积症的超微结构及生化观察及其与泰-萨克斯病和黏多糖贮积症的关系
正常及亚糖尿病兔实验性高胆固醇血症早期中枢神经系统病变
Acta Neuropathol. 1972;22(1):58-67. doi: 10.1007/BF00687550.
4
GM2-gangliosidosis, AB variant: clinico-pathological study of a case.GM2神经节苷脂贮积症,AB变异型:一例临床病理研究
Acta Neuropathol. 1975 Dec 19;33(3):207-26. doi: 10.1007/BF00688395.
5
Progress in investigations of sphingolipidoses.鞘脂类贮积病的研究进展
Acta Neuropathol. 1978 Aug 7;43(1-2):1-18. doi: 10.1007/BF00684994.
J Neuropathol Exp Neurol. 1965 Apr;24:318-40. doi: 10.1097/00005072-196504000-00011.
4
GENERALIZED GANGLIOSIDOSIS: ANOTHER INBORN ERROR OF GANGLIOSIDE METABOLISM?全身性神经节苷脂沉积症:另一种神经节苷脂代谢的先天性缺陷?
Am J Dis Child. 1965 Apr;109:338-46.
5
FAMILIAL NEUROVISCERAL LIPIDOSIS. AN ANALYSIS OF EIGHT CASES OF A SYNDROME PREVIOUSLY REPORTED AS "HURLER-VARIANT," "PSEUDO-HURLER," AND "TAY-SACHS DISEASE WITH VISCERAL INVOLVEMENT".家族性神经内脏脂质沉积症。对先前报告为“胡尔勒变异型”、“假性胡尔勒”和“伴有内脏受累的泰-萨克斯病”的一种综合征的8例病例分析。
Am J Dis Child. 1964 Nov;108:503-22.
6
FINE STRUCTURE OF THE LIPID BODIES IN JUVENILE AMAUROTIC IDIOCY.少年型黑蒙性白痴中脂质小体的精细结构
Acta Neuropathol. 1963 Nov 5;3:144-9. doi: 10.1007/BF00687063.
7
ON THE NATURE OF THE "STORED" LIPID SUBSTANCES IN JUVENILE AMAUROTIC IDIOCY (BATTEN-SPIELMEYER-VOGT).关于青少年黑蒙性白痴(巴滕 - 施皮尔迈尔 - 沃格特病)中“储存”脂质物质的性质
Ann Histochim. 1963 Jul-Sep;8:255-7.
8
Studies in Tay-Sachs disease. II. Ultrastructure of the cerebrum.泰-萨克斯病的研究。II. 大脑的超微结构。
J Neuropathol Exp Neurol. 1963 Jan;22:18-55. doi: 10.1097/00005072-196301000-00003.
9
How cells transform energy.
Sci Am. 1961 Sep;205:62-73. doi: 10.1038/scientificamerican0961-62.
10
Mitochondrial localization of oxidative enzymes: staining results with two tetrazolium salts.氧化酶的线粒体定位:两种四唑盐的染色结果
J Biophys Biochem Cytol. 1961 Jan;9(1):47-61. doi: 10.1083/jcb.9.1.47.