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The enzymic degradation of cerebrosides and sulphatides in human demyelination due to disseminated sclerosis and encephalitis, and to Tay-Sachs disease.

作者信息

Pellkofer R, Jatzkewitz H

出版信息

Acta Neuropathol. 1974;29(1):25-35. doi: 10.1007/BF00684388.

DOI:10.1007/BF00684388
PMID:4440453
Abstract
摘要

相似文献

1
The enzymic degradation of cerebrosides and sulphatides in human demyelination due to disseminated sclerosis and encephalitis, and to Tay-Sachs disease.由于播散性硬化症、脑炎以及泰-萨克斯病导致的人类脱髓鞘中脑苷脂和硫脂的酶促降解。
Acta Neuropathol. 1974;29(1):25-35. doi: 10.1007/BF00684388.
2
Composition of cerebral lipids in murine sudanophilic leucodystrophy: the Jimpy mutant.小鼠嗜苏丹性脑白质营养不良（Jimpy突变体）中脑脂质的组成
J Neurochem. 1970 Jan;17(1):75-83. doi: 10.1111/j.1471-4159.1970.tb00503.x.
3
Hepatic galactosylceramide in globoid cell leukodystrophy (Krabbe's disease).
Lipids. 1973 Mar;8(3):154-6. doi: 10.1007/BF02531813.
4
Biochemical evaluation of a combined sulfatidosis and gangliosidosis (glycolipidosis) of the brain.脑联合硫脂沉积症和神经节苷脂沉积症（糖脂沉积症）的生化评估
Pathol Eur. 1968;3(2):409-15.
5
"SULPHATIDES" AND "NEUTRAL CEREBROSIDES" IN DEMYELINATION.脱髓鞘中的“硫脂”和“中性脑苷脂”
Psychiatr Neurol Neurochir. 1963 Nov-Dec;66:543-8.
6
[Lipoidosis--with special reference to metachromatic leucodystrophy and Tay-Sachs disease].[类脂质沉积症——特别提及异染性脑白质营养不良和泰-萨克斯病]
Nihon Rinsho. 1967 Oct;25(8):1597-606.
7
Metachromatic form of diffuse cerebral sclerosis. V. The nature and significance of low sulfatase activity: a controlled study of brain, liver and kidney in four patients with metachromatic leukodystrophy (MLD).弥漫性脑硬化的异染性形式。五、低硫酸酯酶活性的性质和意义：对四名异染性脑白质营养不良（MLD）患者的脑、肝和肾的对照研究。
Arch Neurol. 1965 Dec;13(6):593-614. doi: 10.1001/archneur.1965.00470060029003.
8
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY. II. CONTROLLED THIN-LAYER CHROMATOGRAPHIC STUDIES OF GLOBOID BODY FRACTIONS IN SEVEN PATIENTS.球形细胞（克拉伯）脑白质营养不良的研究。II. 7例患者球形细胞组分的薄层色谱对照研究。
J Neurochem. 1963 Dec;10:921-30. doi: 10.1111/j.1471-4159.1963.tb11919.x.
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Cerebroside-sulphatase and arylsulphatase A deficiency in metachromatic leukodystrophy (ML).异染性脑白质营养不良（ML）中的脑苷脂硫酸酯酶和芳基硫酸酯酶A缺乏症。
J Neurochem. 1969 Jan;16(1):19-28. doi: 10.1111/j.1471-4159.1969.tb10339.x.
10
[Cerebral lipids in Krabbe's leukodystrophy].[克拉伯病中的脑脂质]
Neurol Neurochir Pol. 1972;6(3):473-7.

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease.患有桑德霍夫病的小鼠、猫和人类大脑脂质的比较分析。
Lipids. 2009 Mar;44(3):197-205. doi: 10.1007/s11745-008-3268-0. Epub 2008 Nov 26.
2
Conversion of labelled cerebrosides in adult rabbit brain, local brain necrosis, autolysis series and in brain homogenate.成年兔脑、局部脑坏死、自溶系列以及脑匀浆中标记脑苷脂的转化。
Acta Neuropathol. 1978 Feb 20;41(2):97-101. doi: 10.1007/BF00689759.

本文引用的文献

1
Protein measurement with the Folin phenol reagent.使用福林酚试剂进行蛋白质测定。
J Biol Chem. 1951 Nov;193(1):265-75.
2
[A NEW METHOD FOR THE QUANTITATIVE ULTRAMICRODETERMINATION OF SPHINGOLIPIDS FROM THE BRAIN].[一种用于定量超微量测定脑内鞘脂类的新方法]
Hoppe Seylers Z Physiol Chem. 1964;336:25-39. doi: 10.1515/bchm2.1964.336.1.25.
3
[DETERMINATION OF C18- AND C24-SPHINGOMYELIN BY THIN-LAYER CHROMATOGRAPHY IN NORMAL AND PATHOLOGICAL BRAINS, INCLUDING A CASE OF NIEMANN-PICK DISEASE].[通过薄层色谱法测定正常及病理大脑中的C18和C24鞘磷脂，包括1例尼曼-匹克病病例]
J Neurochem. 1964 Aug;11:603-11. doi: 10.1111/j.1471-4159.1964.tb11458.x.
4
[On an enzyme from swine kidneys which cleave cerebroside sulfuric acid esters].[关于一种来自猪肾的可裂解脑苷脂硫酸酯的酶]
Hoppe Seylers Z Physiol Chem. 1963 Mar;331:292-4. doi: 10.1515/bchm2.1963.331.1.292.
5
Quantitative carbon-14 and tritium assay of thin-layer chromatography plates.薄层色谱板的碳-14和氚定量测定
Anal Biochem. 1962 Aug;4:128-31. doi: 10.1016/0003-2697(62)90029-5.
6
The assay of arylsulphatases A and B in human urine.人尿中芳基硫酸酯酶A和B的测定。
Clin Chim Acta. 1959 May;4(3):453-5. doi: 10.1016/0009-8981(59)90119-6.
7
Variation of beta-N-acetylhexosaminidase-pattern in Tay-Sachs disease.泰-萨克斯病中β-N-乙酰己糖胺酶模式的变化。
FEBS Lett. 1969 Aug;4(4):351-354. doi: 10.1016/0014-5793(69)80274-7.
8
Cerebroside galactosidase of brain.脑苷脂半乳糖苷酶（存在于脑内）
J Lipid Res. 1966 May;7(3):379-86.
9
Tay-Sachs disease: generalized absence of a beta-D-N-acetylhexosaminidase component.泰-萨克斯病：普遍缺乏β-D-N-乙酰己糖胺酶成分。
Science. 1969 Aug 15;165(3894):698-700. doi: 10.1126/science.165.3894.698.
10
Cerebroside 3-sulfate as a physiological substrate of arylsulfatase A.硫酸脑苷脂作为芳基硫酸酯酶A的生理底物。
Biochim Biophys Acta. 1968 Mar 25;151(3):619-27. doi: 10.1016/0005-2744(68)90008-9.