Wright C B, Lamberth W C, Ponseti I V, Hanson J
Surgery. 1979 Jun;85(6):708-12.
A review of the literature on Ehlers-Danlos syndrome with particular attention to vascular complications enabled us to outline an orderly diagnostic and therapeutic plan which has allowed salvage of an individual with a popliteal false aneurysm. In patients with Ehlers-Danlos syndrome and brachial, superficial femoral, or popliteal arterial disruption, the use of proximal tourniquet control to allow ligation of the disrupted artery under a no-flow, no-pressure situation is recommended. The ligations should be carried out with a large ligature or possibly with large hemoclips and/or reinforced with multiple fine atraumatic vascular sutures distally. These patients may be treated successfully for flexion contractures because of the laxness of their tissues.
对有关埃勒斯-当洛综合征的文献进行回顾，特别关注血管并发症，这使我们能够勾勒出一个有序的诊断和治疗方案，该方案已成功挽救了一名患有腘窝部假性动脉瘤的患者。对于患有埃勒斯-当洛综合征且出现肱动脉、股浅动脉或腘动脉破裂的患者，建议使用近端止血带控制，以便在无血流、无压力的情况下结扎破裂的动脉。结扎应使用大号结扎线，或者可能使用大型血管夹，并/或在远端用多根细小的无创伤血管缝线加强。由于这些患者组织松弛，因此可以成功治疗屈曲挛缩。
