Desai R A, Mahajan V K, Benjamin S, Van Ordstrand H S, Cordasco E M
Chest. 1979 Aug;76(2):170-3. doi: 10.1378/chest.76.2.170.
Three cases of primary intrathoracic amyloidosis are reported. Two of these three patients initially had localized parenchymal pulmonary amyloid tumors (or pulmonary amyloidomas). The third patient developed bilateral enlargement of the hilar lymph nodes as a manifestation of primary amyloidosis. These rare manifestations of primary amyloidosis are illustrated, and their clinical signifiance is discussed. Amyloidoma should be considered in patients with unexplained pulmonary nodules or enlargement of hilar lymph nodes.
报告了3例原发性胸内淀粉样变性病例。这3例患者中有2例最初患有局限性实质性肺淀粉样瘤(或肺淀粉样瘤)。第3例患者出现双侧肺门淋巴结肿大,作为原发性淀粉样变性的一种表现。文中展示了原发性淀粉样变性的这些罕见表现,并讨论了其临床意义。对于原因不明的肺结节或肺门淋巴结肿大患者,应考虑淀粉样瘤。