患有与β地中海贫血相关的镰状细胞贫血的女性的良性产科病史。
Benign obstetric history in women with sickle-cell anaemia associated with -thalassaemia.
作者信息
van Enk A, Lang A, White J M, Lehmann H
出版信息
Br Med J. 1972 Dec 2;4(5839):524-6. doi: 10.1136/bmj.4.5839.524.
Abstract
Two Ghanaian women with sickle-cell anaemia and alpha-thalassaemia were found to have an unusually benign obstetric history. In addition to two factors present which are known to moderate the clinical course of sickle-cell anaemia, good socioeconomic status and a relatively high Hb F level, it is suggested that alpha-thalassaemia may act among other things by lowering the haemoglobin concentration in the red cells and thereby lowering their tendency to sickle in vivo.
摘要
两名患有镰状细胞贫血和α地中海贫血的加纳女性被发现有着异常良好的产科病史。除了已知的两个可缓和镰状细胞贫血临床病程的因素，即良好的社会经济地位和相对较高的胎儿血红蛋白（Hb F）水平外，有人提出α地中海贫血可能通过降低红细胞中的血红蛋白浓度，从而降低其在体内镰变的倾向等方式发挥作用。
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